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A 19-year-old male asked:

Infant suffering from maple syrup disease shouldn't be given food that is containing branched chain amino acids,what are those foods?

2 doctor answers4 doctors weighed in
Dr. John Munshower
Family Medicine 31 years experience
MSUD: Some examples of foods high in protein include all types of meat (e.g., chicken, pork, beef, seafood), all types of dairy (e.g., milk, yogurt, cheese, whipped cream, ice cream, etc.), all types of beans and nuts (e.g., soybeans, pinto beans, peanuts, etc.), and eggs. People with MSUD must also learn what foods have some amount of protein and ways to measure how much. Each individual, depending on the severity of their disorder, is given a daily limit of the protein they can eat. It is okay for people with MSUD to eat some protein because, unlike an allergy, the protein will not cause them to have an "allergic" reaction. In fact, people with MSUD must eat some protein every day as everyone needs some in order to get some leucine, isoleucine and valine for growth and development. The trick is not to eat too much. This is done by learning to count and keep track of the amount they consume throughout the day.
Created for people with ongoing healthcare needs but benefits everyone.
Dr. Neigatha Graney
Pediatrics 38 years experience
Nutrition Specialist: Maple Syrup Urine Disease is a genetic defect. Inability to metabolize branched chain amino acids means dietary proteins must be avoided to prevent brain injury, glucose anomalies & more. Elimination of dietary protein is crucial however the risk of serious nutritional deficits is great without guidance from doctors & nutritional experts. See your doctor for referral to a nutrition specialist.
Created for people with ongoing healthcare needs but benefits everyone.

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Last updated Jul 27, 2014

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