A member asked:

How rare is it to get diagnosed with dandy-walker variant as a child?

4 doctors weighed in across 2 answers
Dr. Alan Ali answered

Specializes in Psychiatry

Dandy Walker : Is a sporadic congenital brain malformation, with incidence of 1 in every 30, 000 live births.

Answered 3/25/2015

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Usually before 1 y/o: 80 to 90 percent of individuals with Dandy-Walker syndrome develop signs and symptoms caused by abnormal brain development within the first year of life. Dandy-Walker syndrome is estimated to affect 1 in 25,000 to 30,000 newborns.

Answered 6/2/2014

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