How long can someone expect to live if they have an untreated pulmonary hypertension?

Third or 4th decade: Progressive untreated primary pulmonary hypertension often reduces the life expectency to 30-40 years of age. In secondary pulmonary hypertension it depends upon the underlying cause, whether that can be treated. Adequately.

Untreated PAH: As pulmonary arterial hypertension (pah) progresses, the increased pressure causes the right side of the heart to enlarge, weaken, and eventually fail. Left untreated, the median survival for pah patients is 2.8 years, and 50 percent of patients diagnosed with pah die within five years. With treatment, progression of pah can be slowed and quality of life maintained; however, the average 5-year sur.