What is the definition or description of: netherton's syndrome?

Skin condition: Netherton syndrome is characterized by chronic skin inflammation, universal pruritus (itch), severe dehydration and stunted growth. Patients with this disorder tend to have a hair shaft defect (trichorrhexis invaginata), also known as "bamboo hair". The disrupted skin barrier function in affected individuals also presents with reddish scaly skin similar to atopic dermatitis.