What is friedrichs ataxia?

Hereditary ataxia: An autosomal dominant disorder causing mitochondrial dysfunction and worsening due to oxidative stress. Spinal disorder usually presenting at a young age, with ataxia, dysarthria, leg weakness, numbness, pes cavus, scoliosis, and cardiomyopathy. Genetic testing for frataxin is confirmatory. There is a variation of ataxia with vitamin E deficiency which is similar, but responds to vit e.