Is hearing loss associated with huntingtons disease my husband has huntingtons and hearing loss. hearing loss before he found out he had hd.

Hearing : Hearing loss is not usually associated with huntington disease. Huntington's disease is progressive degenerative disease of the brain that causes involuntary movements, dementia, and mood disorders. It is caused by a genetic mutation. It is inherited in an autosomal dominant fashion, meaning that children of people with huntington disease have a 50% chance of inheriting the condition. Genetic testing is available.

Dr : Dr krob is correct; huntington's disease is not associated with hearing loss, except perhaps by coincidence as older individuals with hd may also have hearing loss on the basis of other injuries or diseases. Huntington's affects many populations of cells in the nervous system, but is not described to damage the primary hearing sensory cells (hair cells of the inner ear), the acoustic branches of the vestibular nerve, or the brainstem apparatus which transmits information from the inner ear hearing sensors. Huntington's has many effects on cerebral tissues, but does not alter hearing perception or sound interpretation at a cortical level. Some patients with hd have psychiatric issues but I am aware of no reports of hearing loss as a manifestation of behavioral disturbances.