How long do people with primary pulmonary hypertension usually live?

Depends: Primary pulmonary hypertension is a pretty rare disease fortunately. Again, fortunately, over the past several years we have had the introduction of a number of different medications that target pulmonary arterial hypertension (pah) through different pathways. Overall the overall survival of pah patients is still short and in order of a few years usually, dependent on the severity of course.

Depends: There are many factors that influence survival such as age, sex, presence of heart failure, etc. Thus, it is best not to make a general statement before a thorough evaluation. For example, in some studies 85% of patients are alive at two years after diagnosis but if a patient has an episode requiring cpr, only 6% survive two years. Some keys to survival are early diagnosis and treatment.