Gastroenterologist. Your regular doctor can make the initial diagnosis but you probably want to be followed by a gastroenterologist.
No. Primary sclerosing cholangitis is a rare disease affecting 6 out of 100, 000 people in the USA. It is more common in men then in women, and the mean age at diagnosis of is around 40 years of age.
Fatigue, etc. Most people with sclerosing cholangitis are diagnosed based on routine laboratory abnormalities, often without any symptoms. As liver dysfunction progresses, common symptoms include fatigue, jaundice, itching, diarrhea, and (fat-soluble) vitamin deficiency.
Several. Jaundice liver failure sepsis.
Rare. Rare, autoimmune disease...Needs a liver specialist.
Depends. On stage. Usually it has poor response to chronic meds, and antibiotics are used for superimposed infections in times of flare ups.
See below. Complicated for a short answer here. See this site........http://www. Mayoclinic. Org/primary-sclerosing-cholangitis/.
Management of SC. The goal of managing acute attacks is antibiotics and IV fluids. In about 15%, emergency decompression or surgery is needed. Prevention of future attacks of cholangitis is based on removing biliary stones and debris, dilation or resection of strictures, and establishing optimal biliary drainage. Also important to rule out the clonorchis parasite. Your GI doctor can discuss newest treatments.
PSC. Sclerosing cholangitis is a condition that affects the bile ducts and causes strictures. Most patients also have ulcerative colitis. Surgery and even liver transplant may be required to treat the disease.
Inflammation. It is an inflammatory condition of the main bile duct that drains bile from the liver. It is important to follow with an experienced gastroenterologist because untreated, the condition can lead to liver failure.
SC is serious stuff. Acute attacks of cholangitis may be complicated by bacterial infection of bloodstream with shock & abscesses; rupture of pus-filled bile ducts into the abdomen or fistulizing to GI tract, abdominal wall, or heart sac: clotting of the portal vein; or bleeding from the bile duct. Acute pancreatitis occurs in 10% of patients with relapsing disease, & there can be increased risk of bile duct cancer.
PSC is progressive. You do not state whether your sclerosing cholangitis (sc) is primary or secondary, primary sc is an autoimmune disorder where the bile ducts become inflamed, leading to blockage of bile flow leading to liver damage. Secondary sc is due to other type of bile duct injury, but blockage leads to liver damage. Psc is progressive, ssc can only be treated if the blockage is relieved. See a hematologist.
Bile duct obstructio. Idiopathic (probably autoimmune) progressive scarring and narrowing of the bile ducts. May need surgical intervention or transplant This reference may help: http://www. Mayoclinic. Org/diseases-conditions/primary-sclerosing-cholangitis/basics/definition/CON-20029446.