4 doctors weighed in:
How long to people diagnosed with benson's disorder generally live and in what condition? About how many people are believed to have been diagnosed?
4 doctors weighed in

Dr. Peter Kurzweil
Internal Medicine
2 doctors agree
In brief: Few yrs, rare
Benson's syndrome (also posterior-back brain-cortical atrophy) is a rare neurodegenerative disorder start in vision cnter with inability to recognize familiar objects or people.
It is a syndrome, because it can be part of another disease, such as alzheimers or jacob-creutzfeld). Mild to severe, 1 to >10 yrs, stable for yrs or progressive disability. First 2 yrs at specialized center is crucial.

In brief: Few yrs, rare
Benson's syndrome (also posterior-back brain-cortical atrophy) is a rare neurodegenerative disorder start in vision cnter with inability to recognize familiar objects or people.
It is a syndrome, because it can be part of another disease, such as alzheimers or jacob-creutzfeld). Mild to severe, 1 to >10 yrs, stable for yrs or progressive disability. First 2 yrs at specialized center is crucial.
Dr. Peter Kurzweil
Dr. Peter Kurzweil
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Dr. Beth Friedland
Ophthalmology
2 doctors agree
In brief: Not very much known
Benson's disorder (posterior cortical atrophy) is believed to be a visually impairing variant of alzheimer's and is very rare.
See this landmark paper from 2004: http://www.Orpha.Net/data/patho/gb/uk-benson.Pdf a consult with a neuro-ophthalmologist may be helpful.

In brief: Not very much known
Benson's disorder (posterior cortical atrophy) is believed to be a visually impairing variant of alzheimer's and is very rare.
See this landmark paper from 2004: http://www.Orpha.Net/data/patho/gb/uk-benson.Pdf a consult with a neuro-ophthalmologist may be helpful.
Dr. Beth Friedland
Dr. Beth Friedland
Thank
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