What are the surgeries to fix hypoplastic left heart syndrome?

Norwood/Glenn/Fontan. A three-step surgical repair approach has improved outcomes for affected babies, however the intra- and inter-procedure mortality remains significant and the long-term prognosis guarded. See: http://texaschildrens.Org/locate/doctors/ayres, -nancy/.

Related Questions

Is Surgery treatment for Hypoplastic left heart syndrome effective? Drs here (Jordan) said that the surgery can only give the child few extra days?

Complex. Surgery needs to be performed in a highly specialized center for cardiac surgery, it is a complex surgery involving several stages, or ultimately a heart transplant, either way, life long follow up is needed, so unless the funds and other support means are available, as social/emotional support, life won't be easy for the child or the family, good luck. Read more...
Maybe there ? My oldest HLH patient is now a married 27 yo cardiac clinic nurse.Her road to health has been complex, and it was truly the skill of a lot of fine surgeons and cardiologists that kept her going when things looked bad. She was on the transplant list for a while.Thirty years ago, we were at the point where your doctors seem to be. Read more...

What surgeries may be performed on a child with hypoplastic left heart syndrome?

Several. A series of complicated cardiovascular operations are necessary to manage hlhs, with significant intra- and inter-procedure mortality. I think a consultation with an experienced pediatric cardiologist and pediatric cardiovascular surgeon in a center of excellence for congenital heart disease can only answer your questions in truth. http://texaschildrens.org/locate/doctors/ayres, -nancy/. Read more...

Which other surgeries may be performed on a child with hypoplastic left heart syndrome?

HLHS Surgeries. Norwood (stage i) glenn (stage ii) fontan (stage iii) some programs may do a hybrid version of stage i, called the "hybrid stage i". Occasional patients with hlhs will need other procedures depending on their anatomy, but those 3 are the standard surgical treatments. Read more...
See below. There are usually a series of operations that are performed on these children to improve blood flow throughout the body. These patient can also require later surgery to increase the size of the shunts and conduits as the body grows in size. Talk to your surgeon to discuss the future operations that will need to be performed. Read more...

What is hypoplastic left heart syndrome?

A congenital defect. Hypoplastic left heart syndrome (hlhs) is a specific type of congenital heart defect that consists of varying degrees of underdevelopment of the left-sided heart structures including the mitral valve, left ventricle, aortic valve, and aortic arch. Hlhs most likely has a genetic cause and occurs early during fetal development, however the genes involved have not yet been entirely elucidated. Read more...

What cuases hypoplastic left heart syndrome?

Multifactorial. 2-6% recurrence risk with 1-2 prior affected siblings and up to 25% risk with rare familial autosomal recessive forms - both point to genetic underpinnings. The pathological changes center around severe aortic and mitral valve stenoses and hypoplasia/interruption of the aortic arch. Read more...

How is hypoplastic left heart syndrome cured?

It cannot be cured. Hypoplastic left heart syndrome (hlhs) is a congenital defect that occurs early during fetal development and it cannot be cured; babies are born with it. It is possible to treat hlhs with surgical and/or catheter-based therapies, but the anatomic defects cannot be reversed. There are newer fetal interventions under investigation that may improve the outcomes, but they also are not curative. Read more...

In what way is hypoplastic left heart syndrome treated?

Surgery. Typically, a three surgery strategy is pursued. The first stage (norwood) is in the first few days of life. Stage 2 (glenn) is at 4-6 months, and stage 3 (fontan) is at age 2-4 years. The goals of this strategy are to provide reliable blood flow to the lungs and the body and to normalize the workload on the heart. Best results are in specialized congenital heart centers. Read more...

Is? Hypoplastic left heart syndrome usually fatal?

Frequently. At least 20% mortality is expected with this diagnosis. If diagnosed in utero, termination of pregnancy should be offered <24 weeks. A 3-step sequence of major cardiac surgeries is nowadays the standard of care and has fairly good outcomes at experienced centers (norwood/glenn/fontan), with significant intra- and inter-procedural mortality. http://texaschildrens.org/locate/doctors/ayres, -nancy/. Read more...
We all die. My oldest HLS patient is now a 27 yo clinical cardiology nurse. She had a hard road to where she is today, and nothing has come easy, but with superior care and a supportive family she is a survivor. I believe she married last summer. Without treatment these are expected to die in infancy. Read more...

Hypoplastic left heart syndrome, what to do?

Major defect. Limited options & generally fatal in 1st month w/o surgery. First must check for associated conditions: genetic, neurological, other conditions might preclude surgical intervention. Even in ideal candidate, options are generally transplant or staged palliation (series of 3 major surgeries in the first few years of life with a lifetime of care and potential procedures). It's a hard road. Good luck. Read more...