How often does biliary atresia occur and who is more likely at risk?

1/ 10-20, 000 births. The cause of biliary atresia is unknown, although several mechanisms have been implicated including viral infections, genetic causes and toxin exposure.
Uncommon. It occurrs about one in 4500 to 5000 live births. All babies are at risk, although there seem to be some areas of the globe that have a slightly higher incidence.