What is pulmonary fibrosis like?

Scarring. Idiopathic pulmonary fibrosis is an inflammatory process affecting lung parenchyma and resulting in loss of lung storage and resulting in low diffusin capacity and restrictive lung disease. Cardiovascular effect inckude pulmonary hypertension and cor pulmonale. The disease is slowly progressive and unresponsive to all current therapy. Lifespan can be in months(hamman-rich) to a few years.