Biliary atresia treatment?

Kasai procedure. Biliary atresia is most often diagnosed in the neonates. The first line treatment is a surgical procedure called portoenterotomy (kasai) in which a loop of intestine is connected to the liver to act as a conduit for bile drainage in place of the missing bile ducts. The beneficial effects of this procedure, however, is often short-lived many children went on to require liver transplantation.
Surgery. First a patient will have a measurement of bile in blood and looking for conjugated versus unconjugated bile. An ultrasound will be done to look for presence or absence of gallbladder. A hida scan will assess whether bile is being excreted into the intestine. If abnormal the patient will need open liver biopsy , cholangiogram and possible kasai procedure.

Related Questions

What are available treatment options for biliary atresia?

Surgery. Kasai procedure attaches liver to bowel to drian bile. Nutrition support, especially for calories, fats, fat soluble vitamins, zn. May need liver transplant. Read more...
Several. No surgery. Kassi procedure. Liver transplant if kasai does not work or if not performed prior to 60 days of life. Read more...

What happens if the initial treatment for biliary atresia fails?

Liver transplant. If you mean surgery, i.e. Kasai procedure, as "the initial treatment", then liver transplantation is often needed. Untreated, chronic bile buildup leads to cirrhosis and liver failure. Read more...
Transplant. Treatment for biliary atresia is a kasai procedure which should be done before 60 days of life to be effective. One third of patients will do well and be cured. One third will do well for a period of time(years) but will eventually need a liver transplant. The final third will fail kasai and need a liver transplant sooner. Read more...

Is surgery a possible cure for biliary atresia?

Yes. Biliary atresia is an unusual condition usually in newborn babies. Surgery can be used to bypass the blocked bile ducts. Each person and condition is different, and a pediatric surgeon specialist may know what is best. Read more...
Yes. One third of patients can be potentially cured if they get a kasai procedure in timely manner. Read more...
YES. Biliary atresia involves both intra- and extra hepatic bile duct pathology. Standard extrahepatic bypass can provide extended survival for a minority of patients. Liver transplantation provides the only possibility for cure, though it carries with it significant morbidity and mortality. Read more...

What is done for biliary atresia?

Depends on situation. If picked up early enough, some respond to surgery to re-establish bile flow. If operated later than 10 weeks of age, most will need a liver transplant to survive. All cases are quite unique & conferring with the treatment team will provide the best information. Read more...
Surgery. Bonafide biliary atresia requires surgery to confirm diagnosis and treat it. Surgery will involve creating ducts to transport bile from liver to the intestine using an small length of patient's intestine. This is called a kasai procedure. Read more...

What is the disorder biliary atresia?

Bile Duct Blockage. The bile duct carries the bile formed in the liver to the small intestine. Any disease that narrows, scars, or obstructs the duct can be called atresia. In some cases a patient is born with a narrow duct, called congenital atresia. In other cases chronic inflammation, infection, or even rejection of a liver transplant can cause scarring or narrowing of the duct. Read more...
Liver problem. Biliary atresia is a condition in which the bile ducts scar closed and prevent the flow of bile into the intestine. If untreated the liver will die. Surgery is used to biopsy liver do cholangiogram to diagnose the condition and if present a portion of intestine can be fashioned into a replacement for the damaged bile ducts. Read more...
Cong.bile duct block. Biliary atresia is disease of bile ducts in infants.Bile ducts become inflamed,blocked soon after birth.Bile stays in liver,where it starts to destroy liver cells rapidly and cause scarring of liver.No known cause,most likely congenital. Infant gets jaundiced.No cure.Only treatment, surgical anastomosis of the of bowel to liver.Many eventually need liver transplant.Intrahepatic duct blockage worse. Read more...

What are the tests for biliary atresia?

Multiple. Usually start with laboratory tests followed by ultrasound, scintigraphy and biopsy. The gold standard is an operative cholangiogram. Read more...

Describe the features of biliary atresia.?

See below. Jaundice (yellow eyes and skin) is the first sign of ba. The onset occurs any time from birth up to 8 weeks of age, and it is unlikely to appear later. Some infants have pale, gray (acholic) stools. Most infants have dark urine because of bilirubin excretion into the urine. If the jaundice has gone unnoticed and the disease progresses an enlarged liver and spleen may develop. Read more...
Yellow. Biliary atresia causes jaundice in the young infants less than 2 months of age. The type of jaundice needs to be assessed as to the type of bilirubin, direct versus indirect. Elevated direct bilirubin needs to be studies for biliary atresia. A fasting gallbladder ultrasound is done to check for presence of gall bladder. If absent then open liver biopsy is necessary. This is done prior to 60 day ag. Read more...

What is the liver biliary atresia?

Severely narrow duct. We occasionally find infants who appear normal at birth, yet as they get older & grow bigger, the bile (waste) from the liver is unable to get out. The bile ducts are the drainage system for the liver.Arising before or after birth, the drains are to tiny & bile backs up.The infants poo changes from brown to white. Common rx include surgery to unblock ducts or a liver transplant. Read more...
Biliary atresia. Biliary atresia is a congenital scarring of the biliary ducts. These ducts transport bile made in the liver to the intestine so one can digest fats. The ducts scar and obliterate. Bile then cannot exit the liver which poisons the liver. These infants need corrective surgery before they are 2 months old. Read more...