What is the disorder biliary atresia?

Bile Duct Blockage. The bile duct carries the bile formed in the liver to the small intestine. Any disease that narrows, scars, or obstructs the duct can be called atresia. In some cases a patient is born with a narrow duct, called congenital atresia. In other cases chronic inflammation, infection, or even rejection of a liver transplant can cause scarring or narrowing of the duct.
Liver problem. Biliary atresia is a condition in which the bile ducts scar closed and prevent the flow of bile into the intestine. If untreated the liver will die. Surgery is used to biopsy liver do cholangiogram to diagnose the condition and if present a portion of intestine can be fashioned into a replacement for the damaged bile ducts.
Cong.bile duct block. Biliary atresia is disease of bile ducts in infants.Bile ducts become inflamed,blocked soon after birth.Bile stays in liver,where it starts to destroy liver cells rapidly and cause scarring of liver.No known cause,most likely congenital. Infant gets jaundiced.No cure.Only treatment, surgical anastomosis of the of bowel to liver.Many eventually need liver transplant.Intrahepatic duct blockage worse.

Related Questions

Is it likely for me to recieve disability for a chronic liver disease, biliary atresia?

Hard to say. A lot depends on your present health status. Many will do well after a kasai. Some will need liver transplant. Services vary from state to state. Check with you local health department. Read more...

What exactly is biliary atresia?

Birth defect. Malformation and scarrng obliteration of the bile ducts. Starts at birrth and progresses. Any infant who is jaundiced after one month of age needs a bilirubim level and a gallbladder ultrasound. Will need surgical correction prior to 60 days of life. Read more...
Plumbing problem. Think of the issue as if it were the sewer lines in your house.Much of the body's waste is processed in the liver and dumped into bile ducts.It should travel to the common bile duct and be dumped into the intestines.It provides color to the poop.In Billiary atresia, the ducts are too small to empty the bile, and it backs up causing liver damage & jaundice and pale stools. Read more...

What is done for biliary atresia?

Depends on situation. If picked up early enough, some respond to surgery to re-establish bile flow. If operated later than 10 weeks of age, most will need a liver transplant to survive. All cases are quite unique & conferring with the treatment team will provide the best information. Read more...
Surgery. Bonafide biliary atresia requires surgery to confirm diagnosis and treat it. Surgery will involve creating ducts to transport bile from liver to the intestine using an small length of patient's intestine. This is called a kasai procedure. Read more...

Anyone's baby got biliary atresia?

Yes. Several in las vegas. About one third do well. One third will do well for a time and will eventually need a liver transplant. Another third do not benefit from a kasai procedure and go straight to liver transplant. Read more...

What exactly causes biliary atresia?

See below. The causes of biliary atresia are not well established and are probably multifactorial; genetic factors may play a permissive role in some cases, but infectious, toxic, or immunologic mechanisms are probably involved. Read more...
Virus. Theories include in utero infection with parvo type virus that causes the bile ducts to inflame and scar down which results in blockage of bile flow and causes jaundice. Persistence of jaundice causes liver failure and death. Read more...

What are the tests for biliary atresia?

Multiple. Usually start with laboratory tests followed by ultrasound, scintigraphy and biopsy. The gold standard is an operative cholangiogram. Read more...

How is biliary atresia generally treated?

Surgery. Once the diagnosis is made and if the baby is considered an appropriate candidate, the approach is surgical. As the problem is lack of drainage of bile from the liver to the intestine, a new connection is made between the liver and intestine. It is called a portoenterostomy or a kasai procedure. Sometimes the child is not a candidate and may need transplantation of liver. Read more...
Surgery. Biliary atresia is treated by surgery to reconstruct the bile ducts that are missing or obliterated. If done before 60 days of age there is a 33% chance of success. The operation is called a kasai procedure. If unsuccessful, one is looking at a liver transplant. Read more...

Describe the features of biliary atresia.?

See below. Jaundice (yellow eyes and skin) is the first sign of ba. The onset occurs any time from birth up to 8 weeks of age, and it is unlikely to appear later. Some infants have pale, gray (acholic) stools. Most infants have dark urine because of bilirubin excretion into the urine. If the jaundice has gone unnoticed and the disease progresses an enlarged liver and spleen may develop. Read more...
Yellow. Biliary atresia causes jaundice in the young infants less than 2 months of age. The type of jaundice needs to be assessed as to the type of bilirubin, direct versus indirect. Elevated direct bilirubin needs to be studies for biliary atresia. A fasting gallbladder ultrasound is done to check for presence of gall bladder. If absent then open liver biopsy is necessary. This is done prior to 60 day ag. Read more...