What is eagle-barrett syndrome?

Prune-belly syndrome. Prune-belly or eagle-barrett syndrome is a rare form of fetal obstructive uropathy with reported incidence of 1:20, 000-1:50, 000 births. No definite genetic etiology has been determined, although seen 95% in male fetuses. 10% of affected cases have cardiac defects as well. Many affected individuals perish perinatally from lung hypoplasia and kidney failure - not always lethal, though.

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What is eagle-barrett syndrome?

Prune-belly syndrome. Prune-belly or eagle-barrett syndrome is a rare form of fetal obstructive uropathy with reported incidence of 1:20, 000-1:50, 000 births. No definite genetic etiology has been determined, although seen 95% in male fetuses. 10% of affected cases have cardiac defects as well. Many affected individuals perish perinatally from lung hypoplasia and kidney failure - not always lethal, though. Read more...