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Doctor insights on: Why Does Cystic Fibrosis Shorten Life Span

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Why does cystic fibrosis shorten life span?

Why does cystic fibrosis shorten life span?

Chronic Illness: Progress in management has improved the quality of life for CF patients but it doesn't take away the basic vulnerabilities of the illness. In its worst forms, the illness shuts down production of enzymes that permit digestion of food & creates excessive mucous in the lungs that sets them up for deadly pneumonia & lung scaring. At some point, one of the complications will end their life. ...Read more

Dr. William Walsh
992 Doctors shared insights

Cystic Fibrosis (Definition)

A genetic disorder of the lungs and digestive tract. It causes recurrent lung infections and inhibits growth in patients and average life expectancy of patients with cystic fibrosis ...Read more


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What's the average life-span of a female with cystic-fibrosis and diabetes?

What's the average life-span of a female with cystic-fibrosis and diabetes?

Unknown: If you ask many experts they will tell you statistics based on large populations, when you look at an individual its harder to predict. As long as the person takes good care of their diabetes and takes all the medicines for cystic fibrosis and sees the doctor frequently at any sign of infection then the person can live a very long life. ...Read more

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Atypical cystic fibrosis life expectancy?

Atypical cystic fibrosis life expectancy?

Depends: Without a full exam and review of medical records and history of infections secondary to CF would be remiss in trying to become an actuarial. Go see a pulmonologist and discuss the options and likely outcomes. ...Read more

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What is the average life expectancy with cystic fibrosis?

Depends: The life expectancy for a cystic fibrosis (CF) patient depends on a variety of factors. However, in the U.S., the average life expectancy is between 30-40 years of age. ...Read more

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These days what's the life expectancy for people with cystic fibrosis?

Depends...: There is no way to accurately predict how long a person with cystic fibrosis will live, as many different factors affect a person’s health. Severity of disease and time of diagnosis are two such factors. Many people have a mild case of cf, while others can have moderate or severe. In 2009, the median predicted age of survival was in the mid-30s. ...Read more

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What is the life expectancy after a double lung transplant if cystic fibrosis?

What is the life expectancy after a double lung transplant if cystic fibrosis?

Median is 5.5 yrs: That being said, population statistics can't be applied to individuals. How well the surgery went, the match characteristics, how well oh avoid infection, your fitness prior to transplant, how well you tolerate the transplant regimen, etc all effect your quality of life and longevity. ...Read more

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What would be the life expectancy after a double lung transplant if you have cystic fibrosis?

5 to 10 years: 5 year survival after double lung transplant occurs in 80% of people with cf. 10 year survival occurs in 50% of people with CF who have a double lung transplant and therefore is the average life expectancy. Regular medical care to manage episodes of rejection and infection in the transplanted lungs are critical to achieving a good outcome. ...Read more

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Can someone with cystic fibrosis be close to living a "normal" life?

Can someone with cystic fibrosis be close to living a "normal" life?

Not very close!: Good morning,
patients with cystic fibrosis have many difficulties due to recurrent infections and many visits to doctors. Things have changed recently with an aggressive treatment approach provided centers with specialty clinics for management of cf., yet it will far from being close to having a life similar to one without cf. Follow the instructions of the team for the best possible quality. ...Read more

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Can an early cystic fibrosis test rule out the possibility of a late in life diagnosis?

Depends on test: Depending on the original test that was performed, it is unlikely that a diagnosis of CF will be made later in life. Most of the testing that is done today is highly accurate. If you are referring to yourself, at age 31, if the diagnosis of CF has not yet been made, and you have been relatively healthy all of your life, I would say it is unlikely you have it. ...Read more

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How can you expect life to bevfor a person with cystic fibrosis after a lung transplant?

How can you expect life to bevfor a person with cystic fibrosis after a lung transplant?

Varies: Not everyone has a similar experience post lung transplant. In general, respiratory symptoms and breathing, overall improve, and people are able to do activities they were not able to do before as easily. Not all respiratory symptoms go away. Various medications are required and close follow up is mandatory. Survival after lung transplantation is ~ 50% at 5 years. ...Read more

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Does lung transplant improve quality of life for people with cystic fibrosis?

Does lung transplant improve quality of life for people with cystic fibrosis?

Yes: Improvement in quality of life after double lung transplant can be dramatic. Most patients come off of oxygen and have much better quality of life by 6 months after transplant. The improvement after lung transplant can last a long time (years). ...Read more

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How can cystic fibrosis affect p.I.E.S development?

Certainly: Cystic Fibrosis (CF) most common life-limiting genetic disorder of Caucasians, affecting approximately 30K people in the US. A, impacting mainly respiratory function. In recent years patients symptoms better controlled by genetic findings and better medications. Emotional & phys. Development depend on severity, time in hospital, complications. Morb. & mort. Factors afect emotional, cognitive behavior. ...Read more

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Can someone be diagnose with cystic fibrosis in their 40's?

Can someone be diagnose with cystic fibrosis in their 40's?

As a carrier: Genetic carrier testing:
more than 10 million americans are symptomless carriers of the defective CF gene. This blood test can help detect carriers, who could pass CF onto their children. To have cystic fibrosis, a child must inherit one copy of the defective CF gene from each parent. ...Read more

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I have symptoms of cystic fibrosis. Is it possible to start show the symptoms in my 30's?

Yes: Yes it is possible. Presentation of cystic fibrosis varies greatly, and it is possible, depending on your specific mutation (and other factors) to present at a later age. In order to prevent late diagnoses, all states now have a newborn screen in place for cystic fibrosis. ...Read more

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I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

Yes: However, usually an adult who is diagnosed so late has usually had chronic problems with cough and "pneumonias". That said I've diagnosed a new case in a 38 year old woman. ...Read more

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What are the chances of a child getting cystic fibrosis among the different racial groups in the u.S.?

Overall 1/3700: Acording to the CF foundation: the overall birth prevalence is 1/3700. It can occur in any race, however the greatest incidence is in caucasians of northern european descent, being 1/2500. The other major groups affected are hispanics 1/13500, african americans 1/15000.
More than 10 million of us carry one part of the defective gene, but to have the disease you must have a copy from both parents. ...Read more

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How can I know if I have cystic fibrosis?

How can I know if I have cystic fibrosis?

Get tested: Testing for cystic fibrosis starts with a sweat test. If that is abnormal, genetic testing in the blood is used to confirm the diagnosis by finding the specific genetic mutations. In general, people with CF have recurrent pulmonary infections and abdominal discomfort/diarrhea due to fat malabsorption. ...Read more

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How can you get checked for cystic fibrosis?

Sweat test: The best test for cystic fibrosis is a sweat test. Why do you think you need tested? ...Read more

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What can be done for cystic fibrosis sufferers?

Supportive care: CF patients benefit from active coordinated care involving their pcp and a regional cystic fibrosis care center. These are usually part of a children's hospital and involve pediatric pulmonologists and other respiratory care specialists. ...Read more

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What is the cause of cystic fibrosis in general?

What is the cause of cystic fibrosis in general?

Genetic: It is a genetic disease, transmitted by the parents to the kids. ...Read more

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Is good to work outside while having cystic fibrosis?

Is good to work outside while having cystic fibrosis?

CF and environment: Depending on the severity of your cf, leading an active healthy lifestyle outside is not a fantasy. Common sense will dictate avoidance germs by simple hand hygiene (wash, wipe, alcohol base hand gels). Knowing your CF treatment plan as per your pulmonologist/specialist is important for slowing down the progression/maintaining a more resilient defense against bacterial/chronic lung infection. ...Read more

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How likely is it that I am a cystic fibrosis carrier?

About 1 in 25: The likelihood of being a carrier for CF depends on your ethnic background. Among whites it is about 1 in 25 or 30 and in hispanics 1 in 45 or so. It is lower in african americans and asians. If there is a known person in your family with CF that will increase the risk of being a carrier. CF was only known as a disease in 1938, so before that babies died of pneumonia or diarrhea, not cf. ...Read more

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How would I be able to tell if I have cystic fibrosis?

A sweat test: Talk with your doctor about your symptoms. If cystic fibrosis is a concern then a sweat test may help. ...Read more

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Can you be a carrier of cystic fibrosis and not be aware?

Yes, most don't: The carrier state does not affect the health of an individual and is usually discovered only after a carrier couple gives birth to an affected child.It can be picked up by specialized testing. Estimates suggest 5% of caucasions are asymptomatic aarriers of the gene. ...Read more

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What is the definition or description of: cystic fibrosis?

Genetic disorder: Cystic fibrosis is a genetic disorder involving lungs & digestive tract, causing recurrent lung infections due to thick inspissated mucus & poor growth in majority of patients due to malabsorption. Treatment involves inhaled respiratory therapies to prevent lung disease & pancreatic enzymes to enable absorption of nutrients. Average life expectancy is near 40 years, new therapies being developed. ...Read more