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Doctor insights on: Where In The Us Provides The Best Climate For Cf Patients

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Where in the us provides the best climate for CF patients?

Where in the us provides the best climate for CF patients?

Climate & CF: The best outcomes for CF related lung disease are with regular use of airway clearance therapies & inhaled medications, maintaining good nutritional status & closely monitoring for CF related complications at an accredited CF center. Climate will not make any significant difference if you are not doing your prescribed treatments & therapies. Good compliance with therapies will ensure best results. ...Read more

Dr. William Walsh
992 Doctors shared insights

Cystic Fibrosis (Definition)

A genetic disorder of the lungs and digestive tract. It causes recurrent lung infections and inhibits growth in patients and average life expectancy of patients with cystic fibrosis ...Read more


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Could pulmozyme (dornase alfa) use result in increased respiratory rate in non-cf patient with a tracheostomy?

Could pulmozyme (dornase alfa) use result in increased respiratory rate in non-cf patient with a tracheostomy?

Maybe: Side effects with Pulmozyme (dornase alfa) are various and can include irritation of the throat, nose and voice changes. It can also cause hoarseness. I use a fair amount in my patients and have not seen it increase respiratory rate. I guess if it was irritating the airway you could breath faster due to pain/discomfort. I don't think that increased resp rate is very common on this drug. ...Read more

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I was told that pleurodesis makes lung transplant very difficult for cf patients. Is that true?

I was told that pleurodesis makes lung transplant very difficult for cf patients. Is that true?

Operations difficult: Several more recent studies comparing CF patients with pleurodesis and no pleurodesis did not seem to show significant difference in outcome. It was originally though that greater adhesions or fibrosis from pleurodesis would cause excessive bleeding. All patients with CF have some degree of pleural adhesions. Operations can be difficult either way. ...Read more

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Why can't cystic fibrosis patient be near each other?

Increased infection: I am not a pulmonary or infectious specialist so I would defer the definitive answer to those specialty physicians. My understanding is that cystic fibrosis patients have increased risk of pulmonary infection. Placing two individuals with the same increased risk together would increase their risk even more. ...Read more

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Why can't cystic fibrosis patients be near each other?

Why can't cystic fibrosis patients be near each other?

Sharing: Patients with cystic fibrosis are highly susceptible to lung infections. As a result, if they spend a lot of time together, they can readily swap infections. This is one case where you should shun your parents' otherwise good advice on sharing. ...Read more

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What happens in the body of a cystic fibrosis patient?

What happens in the body of a cystic fibrosis patient?

Cystic Fibrosis: There is not enough space to answer this question thoroughly in this format. Check out the link below, it gives some good information on cystic fibrosis and the various systemic effects:
http://en. Wikipedia. Org/wiki/Cystic_fibrosis ...Read more

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What are the caloric needs of patient with cystic fibrosis?

What are the caloric needs of patient with cystic fibrosis?

CF diet/supplements: The caloric needs of a CF patient can be 20-30% higher or more than someone without cf. The use of calories for example in respiratory effort uses calories that would otherwise not be expended.
Eating a high protein high calorie diet along with CF nutritional supplements will help boost caloric intake.
I hope that this helps. ...Read more

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How does cystic fibrosis affect the patient and their family?

Many ways: This is a chronic disease that can cause a variety of consequences to the patient and their family. This is a very complicated question to be answered briefly here. ...Read more

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What does a typical cystic fibrosis patient look like and feel like?

Not clear: Not clear what is being asked. Are you looking for information or looking for a physician for cystic fibrosis? A starting point would be your general physician who can refer you to a specialist, if needed. ...Read more

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What is done to improve the immune system of a cystic fibrosis patient?

Cystic fibrosis: CF is a genetic defect and at this time, it cannot be repaired. Companies such as sangamo pharmaceuticals are working on cures for mono-genetic diseases, and maybe someday a cure could become available. ...Read more

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Is palliative care usually covered by insurance for cystic fibrosis patients?

Is palliative care usually covered by insurance for cystic fibrosis patients?

Should be covered: Palliative care should be covered by insurance, regardless of the underlying diseases a person has. One can call her insurance company to check. Palliative care can be really helpful when a patients diseases can no longer be improved by medical treatments. ...Read more

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Which medications does a cystic fibrosis patient in their mid/late teens take daily?

CF meds: Depends on overall pulmonary and GI status:
if pancreatic insufficient:
-pancreatic enzymes
-cf vitamins
lung disease:
-mucolytics such as pulmozyme
-albuterol-bronchodilator
-chest physiotherapy to clear secretions
-nebulized antibiotics if chronic psuedomonas
-azithromycin if chronic pseudomonas
-anti-inflammatories sometimes
there are also other medications based on disease state. ...Read more

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For what reasons might the pancreas get blocked by mucus in cystic fibrosis patients?

Thick: The secretions in cystic fibrosis are more viscous (thicker) than normal and interfere with normal drainage resulting in blockages of the bronchial tubes of the lung with resultant pneumonia and lung injury. Similar issues involve the pancreas. Newborns with the disease frequently have difficulty passing their bowel movements. ...Read more

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Is it possible to donate a lung to a cystic fibrosis patient if you are a smoker?

Depends: If you are a heavy smoker with significant emphysema you may have reduced your pulmonary reserve to the point that you would have a tough time getting by on one lung, ditto the recipient. You would need to have a full pulmonary function evaluation to find out. ...Read more

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Would it be possible for someone to donate a lung to a cystic fibrosis patient when you are a smoker?

Depends: If your pulmonary function tests show both lungs to have adequate capacity and no significant emphysema then it could be possible. Bear in mind that you both have to be able to live relatively normal lives on the single remaining lung. Both you and the recipient should avoid being in the same room with a cigarette! ...Read more

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Is CBAVD sensitive for Cystic Fibrosis? In other words, if a male patient has both vas deferens, can it be assumed they do not have cystic fibrosis?

Is CBAVD sensitive for Cystic Fibrosis? In other words, if a male patient has both vas deferens, can it be assumed they do not have cystic fibrosis?

Need chromosomal tes: Generally absence of vas deference is associated with cystic fibrosis. However to make a definite diagnosis of caustic fibrosis you need the chromosomal test. ...Read more

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How does gene therapy help a cystic fibrosis patient?

How does gene therapy help a cystic fibrosis patient?

So far not at all: Trying to replace the faulty gene has been a failure so far. The new science of epigenetics tells us that our genes (even "bad" ones) are changed by diet and life style. I havegiven children with CF vitamin supplements. They help greatly but there is no cure. Find a physician who uses nutrient treatment. ...Read more

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Is a high calorie, high fat or high protein diet beneficial to young cystic fibrosis patients?

Is a high calorie, high fat or high protein diet beneficial to young cystic fibrosis patients?

Not high fat: One of the problems folks with CF have is that their pancreatic duct gets blocked. This means that the fat-digesting enzymes from their pancreas can't get to their gut and break down the fat they eat. A high-fat diet would be very bad in this situation. You need to have conversations with your CF doc to optimize your diet. You should have both a pulmonologist and a GI doc on your team. ...Read more

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Does a double lung transplant completely eliminate lung problems for cystic fibrosis patients?

Does a double lung transplant completely eliminate lung problems for cystic fibrosis patients?

It should: Cystic fibrosis is a genetic condition causing significant lung dysfunction. A double lung transplantation replaces the native lungs with supposedly normal lungs, eliminating the problem, but replacing it with problems directly related to transplanted lungs, i.e. Chronic rejection or bronchiolitis obliterans. ...Read more

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Does a successful lung transplant completely get rid of the lung problems for cystic fibrosis patients?

It may: Or you could trade one set of problems for another - even successful lung transplants eventually develop obliterative bronchiolitis after a period of time. Be sure that you meet some post transplant patients who are successful, and compare your quality of life to theirs - if your treatment regimen is oppressive and your lung function is bad enough, you may be better of after a transplant. ...Read more

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What are the risks concerning pregnancy in CF patients?

What are the risks concerning pregnancy in CF patients?

That depends...: I have seen CF patients carry pregnancy to full term. The risk is the same as for anyone with impaired lung function and/or malnutrition (very common problems in CF patients). You should discuss pregnancy with your CF provider, usually a lung doctor, and maybe also a specialist in high risk ob. They can discuss the the risks of pregnancy based on your specific health status. Good luck. ...Read more

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What is the risk concerning pregnancy in CF patients?

What is the risk concerning pregnancy in CF patients?

Cystic fibrosis: This condition is inherited in an autosomal recessive pattern, which means both copies of the gene in each cell have mutations. The parents of an individual with an autosomal recessive condition each carry one copy of the mutated gene, but they typically do not show signs and symptoms of the condition. ...Read more

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What is the best treatment for cystic fibrosis?

Depends: Cystic fibrosis (CF) can affect many organs. The pancreas and lungs are the most commonly and severely affected. It is a rare disease that requires treatment by specialized doctors, ideally through a cystic fibrosis foundation accredited care center. For more info, link to www. Cff. Org. ...Read more

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Which treatment works the best and fastest for cystic fibrosis?

None: There is no best or fastest treatment for cystic fibrosis. It is by far an incurable disease. So far, treatment has been focused upon prevention and treatment of complications. ...Read more

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Where is the best cystic fibrosis lung transplant hospital in the us?

Where is the best cystic fibrosis lung transplant hospital in the us?

Lung Transplantation: There are many lung transplantation centers in the U.S. Among the busiest centers, texas children/s hospital performs many lung transplantations per year. The international society for heart and lung transplantation provides statistical information at ishlt. Org.
It is also important to consider that you will have many follow up visits, so living close to a center may be important as well. ...Read more

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What are the main causes of death for cf?

What are the main causes of death for cf?

Respiratory failure: Respiratory infection leading to respiratory failure is one of the main causes of death in CF ...Read more