Doctor insights on:
Vascular Type Eds
Ehlers-Danlos Syndrome is a medical condition characterized by hypermobile joints, very elastic or stretchy skin that bruises easily, and other abnormalities. It is caused by defects in collagen, an important structural protein that is responsible for the strength of many different types of tissue including skin, ...Read more
Very difficult: True Ehler-Danlos type 4 is characterized by facial changes, translucent skin through which vessels can be seen , easy bruising, and uterine and cardiac problems related to medium and large artery damage. Each event is treatable to some degree, pregnancy is advised against, and some problems require emergency treatment. It is autosomal dominant. With good care one may live long but not normally. ...Read more
Diagnosed with classic ehlers danlos with crossover yesterday & was wondering if blue sclera is associated with all eds types or just vascular type 4?
Older testing: If a comprehensive evaluation is done the people with vascular risk can be determined. The incidence of vascular complications reflects available testing about 15 years ago. With improved testing techniques unanticipated vascular complications are rare without additional risk factors to include smoking. ...Read moreSee 1 more doctor answer
Depends: Would not focus so much on percentages, but instead would present your symptoms to your rheumatologist. Would try to seek out eds centers who understand the condition more than most and have seen a larger volume of eds patients (usually at university hospitals). ...Read moreSee 1 more doctor answer
They test different vessels: They're testing different blood vessels than the ones people with ed have involved. There are different types of blood vessels. Some are different by size, some are different by composition, some are different by function. The ones involved in ed cannot be measured. ...Read moreSee 1 more doctor answer
4 afriend shes in bad shape with vascular eds, in hosp.Dr said she needs to decide future/code status, she has the right at 20 to make own decision rite?
Yes: Very important - every adult needs to decide how he or she wants to leave this world (especially what he or she does not want done) before a severe event or illness happens. That means each adult should write his wishes down, give a copy to his doctor, and give another copy to a family member. Two forms are the advance directive and the polst (physician orders for life-sustaining treatment). ...Read moreSee 1 more doctor answer
Anticoagulants: Vascular ehlers-danlos is a difficult disease to manage. Any of the medications that suppress platelet function, and the anticoagulants generally, need to be avoided. However, of the common over-the-counter medicines, aspirin's by far the most powerful anti-clotting agent; before you receive any other medicine that could make you bleed, your physician would discuss risk-benefit with you. ...Read moreSee 1 more doctor answer
Nitrates/tylenol: Eds pts should avoid nitrates when using eds drugs such as viagra. Children are usually given tylenol (acetaminophen) based on safety over many years. However all forms of analgesics can be use in children depending on the circumstance. All doses will need adjustment. ...Read moreSee 1 more doctor answer