Doctor insights on:
Transposition Great Vessel
A woman that have a surgery on her first day of life of transposition of great vessels can deliver vaginaly?
Hard to say: If you or a specific friend are wondering about childbirth, you/they should first discuss it at length with their docs. The advisability of pregnancy varies with cardiac status & one answer cannot be right for all women. You might want to meet with a geneticist, because there is ~4% risk of CHD in your baby, 10% if dad also has any heart defect. Many with this defect go on to have families, good luck ...Read more
Both cause cyanosis: Both are congenital heart defects that cause cyanosis (less oxygen than normal in the arterial blood.) however, that is the only similarity. In transposition of the great arteries, the primary problem is that the aorta arises from the right ventricle instead of the left ventricle. In t(total)apvr, the primary problem is that the pulmonary veins do not connect directly with the left atrium. ...Read more
How does one differentiate between anomalous pulmonary venous return & transposition of great vessels?
TAPVR vs. TGA: The diagnosis of anomalous venous return (TAPVR) vs. transposition of the great vessels (TGA) is made in the newborn period. Simply put, the TAPVR baby usual presents 'pink' (no blueness) while the TGA baby will appear 'blue'. There are several variations of both TAPVR and TGA. The diagnosis can be accurately diagnosed by transthoracic ECHO and all are surgically operable with excellent results. ...Read more
What exactly is the difference between anomalous pulmonary venous return & transposition of great vessels?
Anomalous pulmonary venous return means taht 1 or more of the pulmonary veins returns blood from the lung to the right atrium instead of the left atrium.
Transposition is a defect where the aorta origninate from the right ventricle and the pulmonary artery comes from the left ventricle which is backwards. ...Read more
How to differentiate between anomalous pulmonary venous return & transposition of great vessels as the underlying disease?
Ultrasound: Pediatric cardiologist use ultrasound (an echocardiogram) to identify the type of congenital heart defect. In anomalous pulmonary venous return, the pulmonary veins do not connect to the left atrium in a normal manner. In transposition of the great arteries, the aorta is connected to the right ventricle and the pulmonary artery is connected to the left ventricle (backwards). ...Read more
Tga: There are 2 types, one D TGA needs immediate surgery in first days of life. Then you have good life expectancy, not necessarily if it is fixed in time. Other is L-TGA or corrected TGA and that one may not ever need surgery, however sometimes needs surgery and sometimes things may go worse since aorta is supported by a weaker ventricle-RV. ...Read more
Arterial vs atrial: When anatomy ideal, hypothermic cardiopulmonary bypass and cardioplegic arrest done, aorta transected, left main and right main coronary buttons made, pulmonary artery transected, lecompte maneuver done, coronary buttons translocated to neoaorta, aorta is anastomosed to left v-a trunk, pulnomary artery anastomosed to reconstructed pulmonary trunk. Atrial switch operation may be required otherwise. Asdcl. ...Read more
ECHO,CATH.,MRI: Echocardiogram diagnostic, emergency cardiac cath for rashking procedure if needed, and to determine coronary anatomy, if a concomitant vsd present, intracavitary pressures and shunt may be determined. Cardiac MRI may be needed for concomitant vascular anomalies and assistance in situs inversus. ...Read more
Tga: open-heart surgery for D TGA type.Get a more detailed answer ›
Cyanosis: This is one of the cyanotic heart defects that leads to a "blue baby". The cause is the poorly oxygenated blood that is circulated to the body. See this link for more info: http://www.Ncbi. Nlm. Nih. Gov/pubmedhealth/pmh0002535/. ...Read more
6 weeks: The most common type of transposition of the great vessels (also known as transposition of the great arteries) is d-transposition or d-tga. Infants with d-tga only are usually discharged from the hospital less than one week following surgery. The often require medication for a few weeks after surgery. The breast bone, which is divided to perform the surgery, fully heals in 6 weeks. ...Read more
See below: Once corrected, there should be no effect on life expectancy. ...Read more
What is the long term prognosis for transposition of the great vessel/ arterial switch done in 1997?
Long term outlook: For Arterial Switch Operation (ASO) is excellent. Long-term outcomes after ASO of greater than 95 percent survival at 20 and 25 years following discharge have been reported from a number of centers. Thanks for trusting HealthTap! ...Read more
2 parallel circ.: It results in 2 parallel circuits. Obviously if baby barely alive some mixing is present. The only crossover connections are the patent ductus arteriosus and the patent foramen ovale or asd. If a vsd present that favors mixing. If the PDA closes and the pfo not big enough, death may ensue unless an emergency rashkind procedure(balloon atrial septostomy) done to allow arteriovenous mixing &oxygenati. ...Read more
Abnormal connections: In tga (transposition of the great arteries) the aorta arises from the right ventricle and the pulmonary artery arises from the left ventricle. In this arrangement, oxygenated blood cannot reach the body, so oxygen delivery to the body is severely impaired. While there are treatments that can stabilize the circulation for a few days, an operation to "switch" the arteries is required as a newborn. ...Read more
Blue newborn!: Tga is a very severe cardiovascular anomaly because it can cause very low oxygen concentration in the blood going to the coronaries and carotids and prove lethal if untreated promptly and expertly. If a ventricular septal defect is present, the newborn can be more stable and interventions can be more planned and less emergent. Fetal life is ok — trouble starts as soon as the cord is clamped. ...Read more
Depends on anatomy: Goal if possible is to achieve, atrioventricular and ventriculoarterial concordance as best possible. Some transpositions of the great arteries are congenitally corrected if baby born with atrioventricular and ventriculoarterial discordance. Is it d or l tga, how many concomitant anomalies are present. If d-tga, no vsd, good valves, no coronary anomalies, good lv and rv, ASD closure and jatene best. ...Read more
Uncommon: The incidence is about 20-30 per 100, 000 live births. ...Read more
Yes and no: There are many genetic syndromes in which a cardiac malformation occurs, including transposition. However, there are other causes as well, such as the fetal effects of maternal diabetes, exposure to substances which can cause birth defects, and reduced folic acid in pregnancy. There are unknown patterns of malformations which we do not understand--heart defects with renal, ear, and vertebral. ...Read more
No: Transposition is a birth defect that occurs in the fetus early as the heart is forming. Tgere is no increased risk because a baby is premature. I am also not aware that tga causes prematurity. ...Read more
A few textbooks state that newborns tend to be large with transposition of the great vessels, but none explain why that is the case?
Diabetic mom: Infants of diabetic moms are at greater risk for congenital anomalies, including heart defects. Infants born to diabetic moms are also more likely to be larger. ...Read more
Does anyone have info on the janene heart operation for transposition of the great vessels? How does it work?
Jatene operation: This procedure is named after the surgeon who pioneered the technique. It is more commonly known as the arterial switch operation, because the transposed great arteries are "switched" back to where they belong. Moving the great arteries is a relatively easy procedure. The more difficult part of the procedure is relocating the coronary arteries, which are very small. ...Read more
Dr. Jatene: Dr. Jatene's operation is used to correct d transposition whenever possible given the proper anatomy present. Coronary buttons are translocated to the neoaorta, the aorta is anastomosed to the left ventricular ventriculoarterial valve, the le compte maneuver is done, the main pulmonary artery is anastomosed to the right ventriculo arterial valve trunk. That's it, the arterial switch procedure. ...Read more
I was born with transposition of the great vessels. I've had 4 open. Heart. Surgeries. I take enalapril and carvedilol. Do you think I qualify for ssi?
Thanks for asking!: It depends on the functional status of your heart. If you had a mustard or senning operation, your right ventricle is pumping to your systemic circulation. This un-natural stress on the right ventricle often leads to heart failure, fatigue, and poor exercise tolerance. If you have these issues you would likely qualify for ssi. ...Read more
When I was born I had a surgery of transposition of great vessels. Now im pregnant so Is it safe for me to have an epidural during delivery?
Shouldn't be issue: After TGA repair, you should still have regular cardiology follow-up, but most neonatal repairs do quite well. If there is no postop coronary artery problem or significant peripheral pulmonary stenosis, then you would typically not need any restrictions or surgical precautions. Again, I would emphasize the need for long term follow-up with a cardiologist with experience with congenital heart dz. ...Read more
Surgery: Initially at birth, medications are provided to prevent closure of the connections between the pulmonary and systemic circulations that are present in fetal life. This allows for some mixing of the oxygenated and un-oxygenated blood and buys time. The ultimate treatment is surgical correction of the defect. ...Read more
Congenital: Transposition of the great arteries is a congenital heart defect, meaning that it is an abnormality of cardiac development and is fully present at birth. Classic, or d-tga refers to a disease where the aorta arises from the rv and the pulmonary artery arises from the lv. Diagnosis is typically made early. Another form of tga (l-tga) is a different disease where the rv and the lv are "inverted. ...Read more
They are unaffected until born .... This is because of the blood circulation system that is in place for the baby while still in utero. It isn't until after birth, that this circulation changes and from "fetal blood circulation" to "adult blood circulation."
Often times, these babies will have heart surgery with in just a few days of being born and go on to live very normal lives. ...Read more