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Doctor insights on: Retroperitoneal Fibrosis In Children

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What is retroperitoneal fibrosis?

What is retroperitoneal fibrosis?

Chronic scarring: Idiopathic retroperitoneal fibrosis is a chronic non-specific inflammation of the retroperitoneum, which can entrap and obstruct important structures, notably the ureters. The average age of diagnosis is about 55 years and the male:female ratio was 3:1. Options for treatment include corticosteroids, other immunosuppressive and hormonal treatment (such as tamoxifen), as well as surgery. ...Read more

Dr. Ana Adelstein
9 Doctors shared insights

Retroperitoneal Fibrosis (Definition)

Retroperitoneal fibrosis is a rare disorder in which the ureters (tubes that bring urine from the kidneys to the bladder) are blocked by a fibrous mass in the area behind the stomach and intestines. It is ...Read more


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Could you treat retroperitoneal fibrosis?

Could you treat retroperitoneal fibrosis?

Difficult: Difficult to treat. Options include surgery, trial of certain medications like Prednisone need multidisciplinary team- surgeons, nephrologists, rheumatlogist. ...Read more

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I'm diagnoised with retroperitoneal fibrosis. Is there a medicine for it and if so what?

I'm diagnoised with retroperitoneal fibrosis. Is there a medicine for it and if so what?

Difficult to treat: Unfortunately, there is little mediation to treat this disorder. Mostly we treat the problems that arise from the fibrosis. Occasionally the fibrosis responds to steroid pulses. Ask your local doc for hematology referral. Be well. ...Read more

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What to do if I have been diagnoised with retroperitoneal fibrosis. Is there a medicen for it if so what?

What to do if I have been diagnoised with retroperitoneal fibrosis. Is there a medicen for it if so what?

Medications: Idiopathic retroperitoneal fibrosis is a chronic non-specific inflammation of the retroperitoneum, which can entrap and obstruct important structures, notably the ureters. Treatment with corticosteroids, alternative treatment strategies for steroid-resistant cases (i.e. intensive immunosuppression) and hormonal treatment, particularly tamoxifen, have been utilized. Surgery may also be indicated ...Read more

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How do docs treat retroperitoneal fibrosis?

How do docs treat retroperitoneal fibrosis?

Manage symptoms: Retroperitoneal fibrosis is one of those chronic disorders without a cure. It causes scarring behind the abdominal organs. Can narrow veins, arteries, urine conduits, ureters. Docs use stents, vacualr bypasses, filters and monitoring to manage the consequences. Long term anticoagulation is often required, as are compression devices for the legs. ...Read more

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What is a renal autotransplant involving retroperitoneal fibrosis & what would be the reason for having this?

What is a renal autotransplant involving retroperitoneal fibrosis & what would be the reason for having this?

Bench Surgery: In retro-pertonial fibrosis, the scar tissue choks the Kidny and ureter results in renal failure, in order to prevent this complication, kidney and ureter is removed and re-implanted in the peritoneal cavity (auto implantation) ...Read more

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Per my medical records for an Ileostomy Reversal surgery I underwent, it states the surgeon did a Renal Autotransplant involving retroperitoneal fibrosis. Normal procedure? Explain, please.

Per my medical records for an Ileostomy Reversal surgery I underwent, it states the surgeon did a Renal Autotransplant involving retroperitoneal fibrosis. Normal procedure? Explain, please.

My take is. ..: This question should be directed to the then surgical team. No one should make a "smart" comment or suggestion now after years from the surgery because how, when, and what should be done in individual procedures for medical calamities have changed and evolved over time. That is life. Let life and medicine evolve and move; it's unfair / un-smart to be a hind-sighted smart one. ...Read more

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What is cystic fibrosis in children from?

What is cystic fibrosis in children from?

Recessive gene: A mutation is carried in the dna of both unaffected parents & that matching or similar mutation is paired up at conception when the sperm & egg form completed chromasomes with the defective info. Late in pregnancy and after delivery, the effect of the CF gene abnormality begins to reveal itself. In carriers, the good gene compensates for the bad & no problems occur. ...Read more

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Can people with cystic fibrosis have children?

Can people with cystic fibrosis have children?

Women can: Men are infertile, but woman can have children, at a serious risk to their health. ...Read more

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How to treat fibrosis post surgical in children?

Can try...: Topical verapamil cream to help reduce fibrosis after surgery. Ask your doctor for a prescription - a good combination is verapamil 10% with diclofenac 5% in transdermal cream. ...Read more

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Is it possible for men with cystic fibrosis to still have children?

Is it possible for men with cystic fibrosis to still have children?

Yes but note:: 1. Cystic fibrosis may affect male fertility through a. Thick viscid semen b. Association with absence of the vas, the tubes that conduct sperm from testes to outside. Thick sperm can be easily handled with iui. Obstruction can be addressed through harvesting sperm from the testes and using it for ivf. 2. Genetic consideration: there is a risk of transmission of CF to children-genetic counseling. ...Read more

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How much time to people with cystic fibrosis live and can it be passed to children?

How much time to people with cystic fibrosis live and can it be passed to children?

Start with this link: The short answer is that CF is genetically passed on to children through inheriting a CF gene from both the mother and the father.
Start with information here:
http://www. Cff. Org/aboutcf/ ...Read more

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Can men with atypical cystic fibrosis have children? I have 2 children, I have no symptoms of CF and I am 32 years old. Never tested for CF.

Can men with atypical cystic fibrosis have children? I have 2 children, I have no symptoms of CF and I am 32 years old. Never tested for CF.

Sometimes: Actually, there are several different reasons that men with classic cystic fibrosis tend to be infertile; CFTR is part of the molecular machinery of spermatogenesis. It depends on your mutation. I'm wondering what you're worried about. Best wishes. ...Read more

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Can pulmonary fibrosis affect young children?

Can pulmonary fibrosis affect young children?

Unusual: Rarely in presence of connective tissue disorders, after certain medications, after chest radiation. ...Read more

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If you mother is a carrier of cystic fibrosis is it posibble for one of her children to get it in there audlt years.?

If you mother is a carrier of cystic fibrosis is it posibble for one of her children to get it in there audlt years.?

Not going to happen: The predominant forms of CF (70%) come from inheriting a delta f508 mutation from both parents. If the biological dad does not carry a CF gene, delta f508 or any of the dozens of similar minor mutations, the kid cannot suddenly develop CF. Carrier detection is available to test any potential parent, and many suggest people know the status of both if one is a known carrier. ...Read more

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My partner has cystic fibrosis (male) and I have children 3 boys to a previous relationship. I'm desperate to know if it possible to have iui?

My partner has cystic fibrosis (male) and I have children 3 boys to a previous relationship. I'm desperate to know if it possible to have iui?

Yes: Of course. Question is whether you are looking for a donor. If so california cryobank takes great care in helping people like you. I'm not sure that IUI with your husbands sperm is a good idea. Check me on this but if you do not carry the gene (1:26 for caucasion, carrier rate) your children may be carriers without the actual disease. Look it up and see geneticist, I'm going off top of head. ...Read more

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How can cystic fibrosis affect p.I.E.S development?

How can cystic fibrosis affect p.I.E.S development?

Certainly: Cystic Fibrosis (CF) most common life-limiting genetic disorder of Caucasians, affecting approximately 30K people in the US. A, impacting mainly respiratory function. In recent years patients symptoms better controlled by genetic findings and better medications. Emotional & phys. Development depend on severity, time in hospital, complications. Morb. & mort. Factors afect emotional, cognitive behavior. ...Read more

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Can someone be diagnose with cystic fibrosis in their 40's?

Can someone be diagnose with cystic fibrosis in their 40's?

As a carrier: Genetic carrier testing:
more than 10 million americans are symptomless carriers of the defective CF gene. This blood test can help detect carriers, who could pass CF onto their children. To have cystic fibrosis, a child must inherit one copy of the defective CF gene from each parent. ...Read more

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I have symptoms of cystic fibrosis. Is it possible to start show the symptoms in my 30's?

Yes: Yes it is possible. Presentation of cystic fibrosis varies greatly, and it is possible, depending on your specific mutation (and other factors) to present at a later age. In order to prevent late diagnoses, all states now have a newborn screen in place for cystic fibrosis. ...Read more

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I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

Yes: However, usually an adult who is diagnosed so late has usually had chronic problems with cough and "pneumonias". That said I've diagnosed a new case in a 38 year old woman. ...Read more

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What are the chances of a child getting cystic fibrosis among the different racial groups in the u.S.?

What are the chances of a child getting cystic fibrosis among the different racial groups in the u.S.?

Overall 1/3700: Acording to the CF foundation: the overall birth prevalence is 1/3700. It can occur in any race, however the greatest incidence is in caucasians of northern european descent, being 1/2500. The other major groups affected are hispanics 1/13500, african americans 1/15000.
More than 10 million of us carry one part of the defective gene, but to have the disease you must have a copy from both parents. ...Read more

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What is residual fibrosis? Is it a severe case?

What is residual fibrosis? Is it a severe case?

Fancy name...: A description for a little bit of scarring following an illness from which you've recovered. I'm sorry the lingo threw you for a loop. Chat with your physician about this if it popped up on a report, and good luck. ...Read more

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I have a minimal right aprical fibrosis. What does that mean?

I have a minimal right aprical fibrosis. What does that mean?

It means: There is an area of scarring in the upper part of your right lung. It could be due to many causes, such as prior infection, but if it is an incidental finding and you are otherwise asymptomatic it may be of no concern. Talk to your doc about the results. ...Read more

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What is vaginal fibrosis and how do you cure it?

What is vaginal fibrosis and how do you cure it?

Vaginal fibrosis: You can think of vaginal fibrosis as bad scar tissue in the vagina. It typically is the side effect of radiation therapy for gynecologic cancers. The vagina looses its elasticity and can shrink. ...Read more

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Hi doctors, can you tell me what is retropertineal fibrosis?

Hi doctors, can you tell me what is retropertineal fibrosis?

Retroperitoneal Fibr: Retroperitoneal fibrosis is a rare disease, often idiopathic, but drugs, infections malignancies, prior surgeries, radiation therapy, smoking, and asbestos exposure have been implicated.. It is characterized by the presence of inflammatory and fibrous retroperitoneal tissue that often encases the ureters & other abdominal organs. Symptoms include back or flank pain, and decreased kidney function ...Read more

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What is cystic fibrosis?

Genetic disorder: It is a genetic disorder characterized by abnormal sodium channels, which affect a great deal of problems including the respiratory and digestive systems. It is most commonly diagnosed in infants failing to gain appropriate weight, and in children who have multiple chronic infections. ...Read more

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What is apical fibrosis?

What is apical fibrosis?

Scarred lung apices: Causes include:

- Sarcoidosis
- eosinophilic pneumonia
- tuberculosis
- cystic fibrosis
- ankylosing spondylitis
- radiation pneumonitis
- pneumoconiosis


...Read more

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Can you die of cystic fibrosis?

Yes but: Yes but with early diagnosis and regular care and adherence to prescribed therapy by a pediatric pulmonologist the long term survival has improved greatly in the past two decades. ...Read more