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Doctor insights on: Primary Pulmonary Hypertension In Children

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What's primary pulmonary hypertension?

What's primary pulmonary hypertension?

High BP in the lungs: High blood pressure (BP) in the lungs is called pulmonary hypertension (ph) or pulmonary arterial hypertension (pah). Pah is considered primary or idiopathic if no clear cause is identified. ...Read more

Dr. Gregory Moneta
324 Doctors shared insights

Hypertension (Definition)

A blood pressure reading has two numbers: a systolic blood pressure and a diastolic blood pressure. The systolic blood pressure is the maximum pressure the blood exerts on the vessels when the heart is beating. The diastolic blood pressure is the pressure the blood exerts on the vessels in between heartbeats. Hypertension, or high blood pressure, begins when the systolic blood pressure remains above 140 or when the diastolic blood pressure remains above 90. Hypertension can be a result of increased blood flow through vessels or increased resistance to ...Read more


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Primary pulmonary hypertension, what to do?

Primary pulmonary hypertension, what to do?

PHAssociation: Check web link phassociation. Org to find pulmonary hypertension expert and center near you for medical evaluation and treatment. ...Read more

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What is primary pulmonary hypertension like?

What is primary pulmonary hypertension like?

PH: High blood pressure in the lungs is called pulmonary hypertension (ph) or pulmonary arterial hypertension (pah). Primary ph is now known as idiopathic (no clear cause) pah which is a chronic and life-changing disease that can lead to breathlessness and right heart failure if left untreated. ...Read more

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What is danger of primary pulmonary hypertension?

What is danger of primary pulmonary hypertension?

Life-threatening: Untreated, it can be fatal. There are many factors that influence survival such as age, sex, presence of heart failure, etc. Thus, it is best not to make a general statement before a thorough evaluation. The key is early evaluation and treatment. ...Read more

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What are the tests for primary pulmonary hypertension?

What are the tests for primary pulmonary hypertension?

Many: There are several tests that a patient goes through to confirm primary pulmonary htn. The process usually begins with an ultrasound of the heart (echocardiogram) to identify high pressure. Other test will include lung function tests, test for blood clots, blood test for a variety of diseases and ultimately a right heart catheterization must be done. ...Read more

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What makes a child get primary pulmonary hypertension?

What makes a child get primary pulmonary hypertension?

Good question: I had a patient with a failure of normal breathing control in brainstem. She had pulmonary hypertension. Thus, I think that enters into the causative mechanism. It may sound strange when I say that it could be something as simple as viamin b1 deficiency, particularly if he craves sugar. I doubt very much that the doc in charge will take that seriously! ...Read more

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What are the symptoms of primary pulmonary hypertension?

What are the symptoms of primary pulmonary hypertension?

Short of breath: The initial symptoms include shortness of breath at exertion which can progress to shortness of breath at rest. Other symptoms can include chest pain and dizziness. In the more advanced stages of the disease the patient will notice leg swell, water retention, rapid heart rates. ...Read more

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How long a primary pulmonary hypertension person can survive.?

This is highly: Variable depending on severity & response to treatment. ..Discuss with your pulmonologist. ...Read more

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Methamphitamines caused primary pulmonary hypertension what's best?

Methamphitamines caused primary pulmonary hypertension what's best?

See a specialist: This is a serious condition and is best handled by a physician who specializes in this condition. ...Read more

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Does anyone have a bad outcome from primary pulmonary hypertension?

Does anyone have a bad outcome from primary pulmonary hypertension?

Yes: Untreated pulmonary hypertension is a life-threatening condition. Medications have been developed that can improve the condition and the outcome. ...Read more

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How long do people with primary pulmonary hypertension usually live?

How long do people with primary pulmonary hypertension usually live?

Depends: There are many factors that influence survival such as age, sex, presence of heart failure, etc. Thus, it is best not to make a general statement before a thorough evaluation. For example, in some studies 85% of patients are alive at two years after diagnosis but if a patient has an episode requiring cpr, only 6% survive two years. Some keys to survival are early diagnosis and treatment. ...Read more

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Are some people more prone to getting primary pulmonary hypertension?

Are some people more prone to getting primary pulmonary hypertension?

It may be inherited: Up to 5% of patients with pulmonary arterial hypertension (pah) may have a genetic or heritable cause. Research studies have identified a genetic abnormality affecting bone morphogenetic protein receptor 2 (bmpr2) that appears to predispose a patient to pah. Fortunately, even if an individual inherits the abnormal gene, the likelihood of developing pah is only 1 in 5. ...Read more

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What happens when a person with primary pulmonary hypertension stops taking drugs?

What happens when a person with primary pulmonary hypertension stops taking drugs?

Bad idea: Untreated pulmonary hypertension is a life-threatening condition. Medications have been developed that can improve the condition and the outcome. ...Read more

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What is the treatment for primary pulmonary hypertension?

What is the treatment for primary pulmonary hypertension?

Vasodilator meds: Treatment of primary pulmonary htn, meaning disease of the pulmonary artery itself, includes medications to lower the BP of the lung blood vessels. The class of meds include prostanoids, endothelin receptor antagonists and phosphodiesterase inhibitors. All of these medication dilated the blood vessel in the lung and lower the pressure. Other medications can include blood thinners and diuretics. ...Read more

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Hi doctors, can you tell me what is primary pulmonary hypertension?

Hi doctors, can you tell me what is primary pulmonary hypertension?

Primary/secondary: When the pressures in the arteries of the lungs are evaluated via left and right heart catheterization, and proven that the increased pressure in the lung circulation is due to the blood vessel problems themselves it is primary. If proven due to other causes as in heart failure, pulmonary embolus, copd, or pulmonary fibrosis then it is secondary. ...Read more

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What is the life expectancy for a person with primary pulmonary hypertension?

What is the life expectancy for a person with primary pulmonary hypertension?

PH Prognosis: Life expectancy for patients with pulmonary hypertension (ph) depends on the type of ph and the severity of the disease. Physicians use the symptoms, bloodwork, exercise capacity, and heart function to determine the severity. ...Read more

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What are meds for primary pulmonary hypertension with a dry cough?

What are meds for primary pulmonary hypertension with a dry cough?

Cough and PH: While dry cough can be a manifestation of pulmonary hypertension (PH) in a small percentage of patients, you should discuss with your doctor other possible causes and treatments. ...Read more

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Are there tests to confirm the doctor's diagnosis of primary pulmonary hypertension?

Are there tests to confirm the doctor's diagnosis of primary pulmonary hypertension?

Echo and cath: Echocardiogram is a good noninvasive tool to evaluate pulmonary hypertension. A right heart cath is a more direct and precise way of measuring pulmonary artery pressure and assesss response to treatment. ...Read more

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Help please? What is medicine for dry cough, patient is suffering from primary pulmonary hypertension?

Help please? What is medicine for dry cough, patient is suffering from primary pulmonary hypertension?

Varies.: See a doctor for management. OTC cough suppressants like Robitussin (guaifenesin) could help with cough. A doctor can prescribe stronger cough medication, follow up on pulmonary hypertension, and check your medications to see if they are causing cough. ...Read more

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Can primary pulmonary hypertension appear/disappear without treatment? 3 yr. At ca. 40 mmHg> down 1 yr. Ca. 25> up 1 yr. 45> now down ca. 25 -by echo

Can primary pulmonary hypertension appear/disappear without treatment? 3 yr. At ca. 40 mmHg> down 1 yr. Ca. 25> up 1 yr. 45> now down ca. 25 -by echo

Two variables: The disease process depends on heart and lungs.
The measuring process... depends on machine, operator, and interpretor. So it is possible. So also other associated disease and medications play a role. ...Read more

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Artrial septial defect with pulmonary hypertension in children?

Artrial septial defect with pulmonary hypertension in children?

Talk to MD: As long as there is no reversal of flow which can happen soon due to pulmonary hypertension, a surgical repair may be beneficial. The answer should be given by a cardiologist. Talk to the cardiologist please for your child's sake. Good luck. ...Read more

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Can children get pulmonary hypertension?

Yes: Sometimes there are congenital cardiac defects that can cause pulmonary hypertension even in newborns. While rare, a pulmonary embolism can cause acquired pah in a child. Primary pah can occur in the teen years. Secondary pH can occur with lung diseases such as cystic fibrosis. ...Read more

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What does severe pulmonary hypertension means?

What does severe pulmonary hypertension means?

Very high pressure: "severe pulmonary hypertension" means that the blood pressure in the lungs is very high. This is different than "systemic hypertension, " which is high blood pressure in the vessels of the body. The concept, however, is the same.

There are a number of causes of this pulmonary hypertension, and when very severe, it can cause significant disease. This should be followed closely by a specialist. ...Read more

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What is the best way to deal with pulmonary hypertension?

Depends: Pulmonary hypertension is classified into five groups. Each group has differing causes, prognosis and response to therapy. ...Read more

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How can I tell if my baby is having pulmonary hypertension?

How can I tell if my baby is having pulmonary hypertension?

Must see a doctor: Children or infants can usually be diagnosed with pulmonary HTN with the help of echocardiography though a heart catheterization is required to confirm the diagnosis. These tests are done when there is clinical suspicion on the part of the treating physicians. ...Read more

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How to know the cause of my moderate pulmonary hypertension?

Pulmonary HTN: If confirmed by a catheter study then there is a differential diagnosis list to assess cause, do not smoke, do drugs, avoid amphetamines etc:go and discuss with whoever made the initial diagnosis ...Read more

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Does pulmonary hypertension affect all races at similar rates?

Does pulmonary hypertension affect all races at similar rates?

Complicated: I'm assuming you're referring to idiopathic or primary pulmonary hypertension? I don't think there has ever been a world wide study - most studies include a registry in their own country, so I don't think the answer to your question is known. There are genetic factors so the incidence may well be different in different races. ...Read more

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What activities must somneone avoid with pulmonary hypertension?

What activities must somneone avoid with pulmonary hypertension?

Discuss with doctor: Limitations for pulmonary HTN could be summarized by "listen to your body". As there are many causes for pulmonary HTN the discussion of activity limitations should be with a physician familiar with the disease. Generally one should avoid salt and should note how quickly the heart rate raises with activity. Certainly actvities in high altitude should be avoided. ...Read more

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What's the difference between hypertension and pulmonary hypertension?

What's the difference between hypertension and pulmonary hypertension?

One is in the lungs: Our blood pressure generally averages around 120/80 although lower is not necessarily bad. When it gets to 130/90 and above this is considered hypertension. The normal pressure in the arteries in the lungs is 25/15 because the right side of the heart only has to push blood through the lungs, not the whole body. When this pressure gets above 35/20 it's pulmonary hypertension. ...Read more

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Is it possible that alagilles syndrome be mistook portal pulmonary hypertension?

Yes: I have not seen one but literature says that it can indeed cause portal hypertension due to the liver problem and blood return is impeded. The smaller pulmonary arteries can be deemed pulmonary hypertension unless left and right heart cath can be done to prove the pulmonary circulation is ok and only the larger artery involved, cath may be difficult due to the pressure and size of vessels. ...Read more

Dr. Charles Burger
314 Doctors shared insights

Pulmonary Hypertension (Definition)

Elevated blood pressure in the lungs that can be a primary problem or due to other causes. The right side of the heart pumps blood to the lungs and if the blood pressure in the lungs is elevated, the right side of the heart can fail. Pulmonary hypertension can be difficult to diagnose and usually requires echocardiography ...Read more


Dr. Robert Boswell
42 Doctors shared insights

Primary Pulmonary Hypertension (Definition)

Primary pulmonary hypertension is a condition of increased pressure in the blood vessels of the lung, often leading to weakness, shortness of ...Read more