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Doctor insights on: Left Hypoplastic Heart Disease

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What cuases hypoplastic left heart syndrome?

What cuases hypoplastic left heart syndrome?

Multifactorial.: 2-6% recurrence risk with 1-2 prior affected siblings and up to 25% risk with rare familial autosomal recessive forms - both point to genetic underpinnings. The pathological changes center around severe aortic and mitral valve stenoses and hypoplasia/interruption of the aortic arch. ...Read more

Dr. Bennett Werner
2,804 doctors shared insights

Heart Diseases (Definition)

Heart disease is a condition in which a person has problems within his or her vascular system and heart, which includes both congenital birth defects and problems acquired later. Examples of heart disease include clogging (atherosclerosis) of the coronary (heart) arteries, heart attacks (obstructions of the arteries), damaged heart valves, heart muscle failure, and viral infections of the heart. Some major causes of heart disease include genetics, smoking, hypertension, high ...Read more


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What is hypoplastic left heart syndrome?

What is hypoplastic left heart syndrome?

A congenital defect: Hypoplastic left heart syndrome (hlhs) is a specific type of congenital heart defect that consists of varying degrees of underdevelopment of the left-sided heart structures including the mitral valve, left ventricle, aortic valve, and aortic arch. Hlhs most likely has a genetic cause and occurs early during fetal development, however the genes involved have not yet been entirely elucidated. ...Read more

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Is ?Hypoplastic left heart syndrome genetic?

Is ?Hypoplastic left heart syndrome genetic?

Yes - multifactorial: 2-6% recurrence risk with 1-2 prior affected siblings and up to 25% recurrence risk in familial autosomal recessive rare cases. ...Read more

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Is ?Hypoplastic left heart syndrome usually fatal?

Is ?Hypoplastic left heart syndrome usually fatal?

Frequently.: At least 20% mortality is expected with this diagnosis. If diagnosed in utero, termination of pregnancy should be offered <24 weeks. A 3-step sequence of major cardiac surgeries is nowadays the standard of care and has fairly good outcomes at experienced centers (norwood/glenn/fontan), with significant intra- and inter-procedural mortality. http://texaschildrens.org/locate/doctors/ayres, -nancy/. ...Read more

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How is hypoplastic left heart syndrome diagnosed?

How is hypoplastic left heart syndrome diagnosed?

Ultrasound + cath: The DX is possible from a cardiac ultrasound & a cardiac cauterization. ...Read more

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How is hypoplastic left heart syndrome cured?

How is hypoplastic left heart syndrome cured?

It cannot be cured: Hypoplastic left heart syndrome (hlhs) is a congenital defect that occurs early during fetal development and it cannot be cured; babies are born with it. It is possible to treat hlhs with surgical and/or catheter-based therapies, but the anatomic defects cannot be reversed. There are newer fetal interventions under investigation that may improve the outcomes, but they also are not curative. ...Read more

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What causes hypo-plastic left heart syndrome?

What causes hypo-plastic left heart syndrome?

Genetic defect : This is generally caused by a genetic defect and is exceedingly rare. ...Read more

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What is hypoplastic right heart syndrome?

What is hypoplastic right heart syndrome?

Hypoplastic Right: A congenital heart abnormality with an underdeveloped right atrium and ventricle. ...Read more

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Small left sided heart with abnormal septal motion in ventricle EF 60-65% heart is normal including thickness. Possible pulmonary hypertension cause?

Small left sided heart with abnormal septal motion in ventricle EF 60-65% heart is normal including thickness. Possible pulmonary hypertension cause?

MRI: If you have severe pulmonary hypertension, you may have Primary Pulmonary Hypertension. This is potentially a serious diagnosis. Intracardiac and intrapulmonary shunting must be ruled out. A cardiac MRI and nuclear shunt test can make this determination. These tests are likely only available at a major referral center - London. Good luck. ...Read more

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What is the relationship between coronary artery disease, coronary heart disease and ischemic heart disease?

What is the relationship between coronary artery disease, coronary heart disease and ischemic heart disease?

Same: Basically similar names for the same problem. Each discribes a problem with the circulation of the heart the cornary arteries. ...Read more

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Would left coronary artery blockage produce ischemia of left ventricle and right axis deviation on ekg?

Would left coronary artery blockage produce ischemia of left ventricle and right axis deviation on ekg?

It could: you should discuss this with your doctor to see how severe the ischemia is and w to manage it ...Read more

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What is the relationship between coronary artery disease, coronary heart disease, and ischemic heart disease?

What is the relationship between coronary artery disease, coronary heart disease, and ischemic heart disease?

All related: Ischemic heart disease is caused by coronary artery disease. Some people call coronary artery disease coronary heart disease. When a coronary artery closes up, the heart tissie it supplied may die and that is called a heart attack. The dead heart tissue scars down, when there is a lot of damaged tissue the heart may start failing and that is called ischemic heart disease. ...Read more

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Bicuspid heart valve disease causes?

Bicuspid heart valve disease causes?

Generally yes: With aging, other factors become superimposed such as onset of coronary disease, hypertension, and senescent changes in diastolic function. Moreover, the involved valve itself may gradually deteriorate. The net effect is often progressive worsening but this may not be noticed since people tend to slow down and do less activity as they age. ...Read more

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What's mean mild coronary artery disease involving the left anterior descending and the right coronary artery? It's something to worry? Heart attack?

What's mean mild coronary artery disease involving the left anterior descending and the right coronary artery?  It's something to worry? Heart attack?

MDs visual judgement: I would be quite wary of the assessment, likely based on a coronary angiogram. Get a copy of all the images, on a cdrom from hospital, &closely examine yourself. Do not settle for someone else's interpretation, its not their body/heart. Any narrowing (stenosis) means advanced atherosclerosis with previous plaque ruptures; clots which have fibrosed/not-cleared; narrowed the opening of the artery. ...Read more

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What syndrome has hypoplastic ventricle, pulmonary and tricuspid atresia?

What syndrome has hypoplastic ventricle, pulmonary and tricuspid atresia?

Variable: Could be a dorv double outlet right ventricle which can incorporate the defects mentioned. ...Read more

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Left neck vein bulges. Is that left heart failure?

Left neck vein bulges. Is that left heart failure?

Probably not: First, neck vein distension can be caused by many things, only one of which is heart failure. Second, if it were due to heart failure, it would likely be on both sides, and then would reflect problems on the right heart. But since the most common cause of right heart failure is left heart failure, neck vein distension is a sign of heart failure. But not likely in you. Talk to your own doctor. ...Read more

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Hypoplastic left heart syndrome, what to do?

Hypoplastic left heart syndrome, what to do?

Major defect: Limited options & generally fatal in 1st month w/o surgery. First must check for associated conditions: genetic, neurological, other conditions might preclude surgical intervention. Even in ideal candidate, options are generally transplant or staged palliation (series of 3 major surgeries in the first few years of life with a lifetime of care and potential procedures). It's a hard road. Good luck. ...Read more

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How does left-sided heart failure cause right-sided heart failure?

How does left-sided heart failure cause right-sided heart failure?

CHF: the failed left ventricle backs blood up in the lungs which increases the work of the right heart which eventually fails ...Read more