Doctor insights on: Is pulmonary fibrosis the same as cystic fibrosis
No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more
No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more
Involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways.
Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more
No: The lungs retain the genetically determined structure of the donating person. ...Read more
Sodium channel: Cystic fibrosis or CF is a genetic disorder that affects a sodium channel (salt) in the lining of the airways, sinuses and other organs. With this abnormality salt and water leave the lumen (center) of the airways resulting in thickening of secretions and airways congestion/pneumonia and poor function. ...Read more
Cilia, hydration, Rx: Mucus lubricates and protects the linings of the airways, digestive system, reproductive system, and other organs and tissues. But in cystic fibrosis, it is abnormally thick and sticky. Thus, it can obstruct the airways, etc. Keeping well to over hydrated, ned's like mucormyst, abx when appropriate can help. ...Read more
Mucus & infection: The cells lining the airways don't put out enough water into the airway to make airway secretions thin enough to be coughed out. The mucus that collects clog the airways and let germs grow and thrive instead of being killed. Long-term infection damages the airways and substance of the lung. The airways and lung units gradually fill up with pus and germs and can't take in oxygen or get rid of co2. ...Read more
Possible but small %: Many people with cystic fibrosis have aspergillus (a fungus) in their airway, but in the vast majority of cases it does not cause disease. In a small percent of patients it may cause allergic bronchopulmonary aspergillosis (abpa), and that can lead to lung damage. Abpa can usually be treated. ...Read moreSee 1 more doctor answer
I have cystic fibrosis but I'm wondering about trying a joint (weed) once. Will it effect my lungs/health?
Not a good idea: Depending on your specific disease situation smoking a joint once may or may not affect your lungs. Having CF often leads to lung inflammation and lung damage to start with. The last thing you want to do is exacerbate those by smoking (cigarettes or marijuana). ...Read moreSee 1 more doctor answer
Hi I suffer with cystic fibrosis and I also have MRSA in the lungs and I was wondering if it is possible that I can get tattoos..
Be cautious: Speak with your pulmonologist who is most familiar with your current status for clearance, but Pseudomonas colonization in the lungs should not usually prevent you from having procedures performed on your skin. You have listed MRSA as one of your conditions, which may put you at much higher risk for severe skin infection from a tattoo. ...Read more
If I have cystic fibrosis and get a lung transplant, will the disease eventually invade my new lungs?
There are chloride ion channel drugs for the gut. Are there any for the lungs for people with cystic fibrosis?
Yes: Medications for the chloride channels in CF function anywhere the body has the channels. ...Read more
When babies are born, are they screened for cystic fibrosis? Also, can a chest xray indicate cystic fibrosis in the lungs?
Depends: The specifics of newborn screening are defined on a state to state basis. Many states screen for CF, but this was not added to the screening in my state until about 10 years ago. The x-ray changes that may be seen in some older CF patients are not present in early childhood and not specific to the disease when they are seen. ...Read moreSee 1 more doctor answer
I have very thick mucus from my lungs, nose, and even vagina (>1yr) Is it possible to have cystic fibrosis and not be diagnosed until adulthood?
Possible: If you have significant concerns about persistent lung congestion and excessive mucus production, frequent sinus infections, consult a pulmonologist for testing and advice. Mild or atypical cases of cystic fibrosis may not be diagnosed until adulthood. ...Read moreSee 2 more doctor answers
What do you advise if I'm wondering how exactly cystic fibrosis could be cured through gene therapy. Would the cells in only the lungs be treated?
Start with this link: Http://cystic-fibrosis. Emedtv. Com/cystic-fibrosis/cystic-fibrosis-gene-therapy. HtmlGet a more detailed answer ›