Doctor insights on:
Is Pulmonary Fibrosis The Same As Cystic Fibrosis
Cystic fibrosis is a genetic disorder involving lungs & digestive tract, causing recurrent lung infections due to thick inspissated mucus & poor growth in majority of patients due to malabsorption. Treatment involves inhaled respiratory therapies to prevent lung disease & pancreatic enzymes to enable absorption of nutrients. Average life expectancy is near 40 years, ...Read more
No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more
No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more
Mucus & infection: The cells lining the airways don't put out enough water into the airway to make airway secretions thin enough to be coughed out. The mucus that collects clog the airways and let germs grow and thrive instead of being killed. Long-term infection damages the airways and substance of the lung. The airways and lung units gradually fill up with pus and germs and can't take in oxygen or get rid of co2. ...Read more
Possible but small %: Many people with cystic fibrosis have aspergillus (a fungus) in their airway, but in the vast majority of cases it does not cause disease. In a small percent of patients it may cause allergic bronchopulmonary aspergillosis (abpa), and that can lead to lung damage. Abpa can usually be treated. ...Read moreSee 1 more doctor answer
Sodium channel: Cystic fibrosis or CF is a genetic disorder that affects a sodium channel (salt) in the lining of the airways, sinuses and other organs. With this abnormality salt and water leave the lumen (center) of the airways resulting in thickening of secretions and airways congestion/pneumonia and poor function. ...Read more
Cilia, hydration, Rx: Mucus lubricates and protects the linings of the airways, digestive system, reproductive system, and other organs and tissues. But in cystic fibrosis, it is abnormally thick and sticky. Thus, it can obstruct the airways, etc. Keeping well to over hydrated, ned's like mucormyst, abx when appropriate can help. ...Read more
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