Doctor insights on:
Idiopathic Pulmonary Fibrosis In Children
How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.
Sorry to hear that. It is a very bad disease with loss of lung function. Being what ultimately causes someone in that situation to die. (transplant?).
Not able to keep the oxygen up, or accumulation of fluid behind the lungs, or a cold/upper respiratory infection, or not being able to breathe out the bad air. With all but the last, not being able to breathe is the bad sign. ...Read more
Lung condition: Ipf is a dangerous condition where scar tissue replaces normal lung tissue choking off normal air units and causing breathlessness. It is a progressive disease with no effective treatment at present. ...Read more
Some forms are: A few rare forms of ipf have been identified and defective genes identified, but this is not the case for th majority of ipf sufferers. There may be a heritable genes for the disease, but they have not been identified. ...Read more
Scarring...: Idiopathic pulmonary fibrosis means that there is scarring of the lungs and the underlying reason for the scarring is not known. It is typically a slowly progressive disease, typically over years. At the final stages, consideration of a lung transplant can be made so avoid smoking to ensure that you would be a candidate, if it progresses to that stage. ...Read more
Yes: Ipf is a relatively rare disorder, particularly if the diagnosis has been confirmed. There is a lot of support online, including the pulmonary fibrosis foundation. Look it up! ...Read more
Not yet: Unfortunately, no effective treatment for ipf is known. Currently, using n-acetyl- cysteine and possibly an experimental drug called perfenidone may be of benefit; they are not cures or even effective at reversing or arresting progression of disease. ...Read more
Shortness of breath: Temperature extremes are harmful because pulmonary fibrosis prevents adapting to the increased metabolic needs that occur with either cold or hot temperatures. Increased dyspnea (shortness of breath) is the typical consequence. The heart can also be strained because it is under more strain in pulmonary fibrosis. ...Read more
What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?
Possible: Some people with ipf can get affected by the cold weather. It really depends on the individual. Usually, during the cold weather, the increase in respiratory viruses (especially flu) can cause trouble in patients with any sort of lung disease. But, it really depends on the individual. ...Read more
No good treatemtns:
Unfortunately, there are no good, effective treatments for idiopathic pulmonary fibrosis. Many have been tried, such as steroids, anti-inflammatory drugs, and a drug called mucomyst, (acetylcysteine) but the studies done have not shown significant efficacy.
Treatment is mainly supportive. ...Read more
None effective: Unfortunately there are no effective treatments for ipf. Currently n-acetyl cysteine and perfenidone are being studied, but at this time no effective treatment has been found. ...Read more
Discuss with : Your doctor. Impossible to know with limited info. ...Read more
Depends on level: If your oxygen level, on room air, is over 90% at rest and with walking, you won't need oxygen. In fact, you won't even qualify for oxygen therapy at home until your level goes down to 88%. Thus, simply having that diagnosis of ipf doesn't necessarily mean you will need oxygen. Now, many people with ipf do need oxygen, but it doesn't necessarily need so. ...Read more
Depends: The average life expectancy is 3 to 5 years however there are many factors that could change that. For example what stage you are in now. Other diseases you may have, diet, and smoking are a few of the factors that contribute to ur prognosis. There are 2 pulmonary fibrosis meds, Ofev and Esbriet that may help you. Pulmonary rehaTalk with ur lung doctor and see where you stand. Good luck ...Read more
No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more
There aren't many...:
Unfortunately, there are not many treatments for idiopathic pulmonary fibrosis that have been shown to work. Mainly, the focus is on comfort and symptom management.
Sometimes, oxygen can be of benefit. I would also get him evaluated for pulmonary rehab. Although there is no cure, there are many people who can live a long time with ipf. It depends on how bad it is. He should def. See a lung doc. ...Read more
No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more
Involves large amounts of mucus in the airways. Therefore, it is difficult for air to flow due to mucus obstructing airways.
Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more
Kindly guide me how to handle idiopathic pulmonary fibrosis, diagnosed in my mom. She is suffering from dry cough now, and feels fatigued while walk.
Help is available:
The coalition for pulmonary fibrosis can provide guidance, education and support for families and patients dealing with pulmonary fibrosis. There website is: http://www.Coalitionforpf. Org/
This is a challenging diagnosis--you are not alone. ...Read more
My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?
Lung transplant: Other factors are considered too, as age, general health, other chronic diseases, the original lung disease and whether it can recur in the transplanted lung, your father needs to be evaluated in a tertiary care hospital, either a university or a teaching hospital, better if they have a transplant program, wish you and your father wellness ...Read more