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Doctor insights on: Idiopathic Pulmonary Fibrosis In Children

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How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.

How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.

Sorry: Sorry to hear that. It is a very bad disease with loss of lung function. Being what ultimately causes someone in that situation to die. (transplant?).

Not able to keep the oxygen up, or accumulation of fluid behind the lungs, or a cold/upper respiratory infection, or not being able to breathe out the bad air. With all but the last, not being able to breathe is the bad sign. ...Read more

Idiopathic (Definition)

An idiopathic medical condition is one of unknown or obscure cause. In some conditions, there may be known causes as well. For example, themajority of glaucoma cases are idiopathic (unknown cause), but there are some cases related to eye ...Read more


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What is idiopathic pulmonary fibrosis?

What is idiopathic pulmonary fibrosis?

Lung condition: Ipf is a dangerous condition where scar tissue replaces normal lung tissue choking off normal air units and causing breathlessness. It is a progressive disease with no effective treatment at present. ...Read more

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Can idiopathic pulmonary fibrosis be treated?

Can idiopathic pulmonary fibrosis be treated?

Pirfenidone: Not approve in the us, yet

approved in europe and japan

But not very powerful, unfortunately. ...Read more

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What are the tests for idiopathic pulmonary fibrosis?

What are the tests for idiopathic pulmonary fibrosis?

CT or biopsy: The "gold standard" test for idiopathic pulmonary fibrosis is a lung biopsy, usually via lung surgery. But, nowadays, ct scan has gotten very good at diagnosing ipf, and sometimes this is enough. But, usually, lung biopsy is required to make a diagnosis. ...Read more

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What are the symptoms of idiopathic pulmonary fibrosis?

Shortness of breath: Slowly progressive shortness of breath, chest discomfort, cough with exercise, declining exercise capacity. At advanced stages weight loss leg swelling frank chest pain simulating angina. ...Read more

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Is it true that idiopathic pulmonary fibrosis hereditary?

Is it true that idiopathic pulmonary fibrosis hereditary?

Some forms are: A few rare forms of ipf have been identified and defective genes identified, but this is not the case for th majority of ipf sufferers. There may be a heritable genes for the disease, but they have not been identified. ...Read more

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What does it mean when idiopathic pulmonary fibrosis found?

What does it mean when idiopathic pulmonary fibrosis found?

Scarring...: Idiopathic pulmonary fibrosis means that there is scarring of the lungs and the underlying reason for the scarring is not known. It is typically a slowly progressive disease, typically over years. At the final stages, consideration of a lung transplant can be made so avoid smoking to ensure that you would be a candidate, if it progresses to that stage. ...Read more

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Is it rare to suffer from idiopathic pulmonary fibrosis (ipf)?

Is it rare to suffer from idiopathic pulmonary fibrosis (ipf)?

Yes: Ipf is a relatively rare disorder, particularly if the diagnosis has been confirmed. There is a lot of support online, including the pulmonary fibrosis foundation. Look it up! ...Read more

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What are the end life symptoms of idiopathic pulmonary fibrosis?

What are the end life symptoms of idiopathic pulmonary fibrosis?

Shortness of breath: Progressive shortness of breath and inability to sustain normal o2 levels are common end of life symptoms. Sometimes the right side of the heart fails causing lots of leg swelling and fatigue. ...Read more

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Are there any ways to suppress/treat idiopathic pulmonary fibrosis?

Not yet: Unfortunately, no effective treatment for ipf is known. Currently, using n-acetyl- cysteine and possibly an experimental drug called perfenidone may be of benefit; they are not cures or even effective at reversing or arresting progression of disease. ...Read more

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Would being exposed to extreme temperatures affect someone with (idiopathic) pulmonary fibrosis?

Shortness of breath: Temperature extremes are harmful because pulmonary fibrosis prevents adapting to the increased metabolic needs that occur with either cold or hot temperatures. Increased dyspnea (shortness of breath) is the typical consequence. The heart can also be strained because it is under more strain in pulmonary fibrosis. ...Read more

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What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?

What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?

Possible: Some people with ipf can get affected by the cold weather. It really depends on the individual. Usually, during the cold weather, the increase in respiratory viruses (especially flu) can cause trouble in patients with any sort of lung disease. But, it really depends on the individual. ...Read more

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Could being exposed to extreme temperatures have any effect on someone with (idiopathic) pulmonary fibrosis?

In general no.: Exposure to extremes of temperatures is unlikely to have an effect on ipf per se. Though other physiological effects of extremes of temperature can compound the sense of shortness of breath. ...Read more

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What is the treatment for idiopathic pulmonary fibrosis?

What is the treatment for idiopathic pulmonary fibrosis?

No good treatemtns: Unfortunately, there are no good, effective treatments for idiopathic pulmonary fibrosis. Many have been tried, such as steroids, anti-inflammatory drugs, and a drug called mucomyst, (acetylcysteine) but the studies done have not shown significant efficacy.

Treatment is mainly supportive. ...Read more

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What is the treatment for idiopathic pulmonary fibrosis?

None effective: Unfortunately there are no effective treatments for ipf. Currently n-acetyl cysteine and perfenidone are being studied, but at this time no effective treatment has been found. ...Read more

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How often should I use oxygen if I have idiopathic pulmonary fibrosis?

How often should I use oxygen if I have idiopathic pulmonary fibrosis?

24hr a day: If you need oxygen, your doctor will let you know, usually round the clock. Best is to get a device that measures oxygen level called oximeter, and keep oxygen saturation above 88%. ...Read more

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Please help, how much or how often should I use oxygen if I have idiopathic pulmonary fibrosis?

Please help, how much or how often should I use oxygen if I have idiopathic pulmonary fibrosis?

Depends on level: If your oxygen level, on room air, is over 90% at rest and with walking, you won't need oxygen. In fact, you won't even qualify for oxygen therapy at home until your level goes down to 88%. Thus, simply having that diagnosis of ipf doesn't necessarily mean you will need oxygen. Now, many people with ipf do need oxygen, but it doesn't necessarily need so. ...Read more

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What is the prognosis for idiopathic pulmonary fibrosis in a 66-year-old male?

What is the prognosis for idiopathic pulmonary fibrosis in a 66-year-old male?

Depends: The average life expectancy is 3 to 5 years however there are many factors that could change that. For example what stage you are in now. Other diseases you may have, diet, and smoking are a few of the factors that contribute to ur prognosis. There are 2 pulmonary fibrosis meds, Ofev and Esbriet that may help you. Pulmonary rehaTalk with ur lung doctor and see where you stand. Good luck ...Read more

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Are there any treatments to cure idiopathic pulmonary fibrosis?

Unfortunately no. : Unfortunately, there is no real cure. There are still attempts to treat symptoms with bronchodilators, and we will give steroids a try, but overall immunosuppressants don't work. If it gets bad enough, transplant is sometimes an option. ...Read more

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Are idiopathic pulmonary fibrosis cystic fibrosis the same?

No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more

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My uncle has idiopathic pulmonary fibrosis, please suggest treatment?

My uncle has idiopathic pulmonary fibrosis, please suggest treatment?

There aren't many...: Unfortunately, there are not many treatments for idiopathic pulmonary fibrosis that have been shown to work. Mainly, the focus is on comfort and symptom management.

Sometimes, oxygen can be of benefit. I would also get him evaluated for pulmonary rehab. Although there is no cure, there are many people who can live a long time with ipf. It depends on how bad it is. He should def. See a lung doc. ...Read more

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Can you let me know is idiopathic pulmonary fibrosis the same as cystic fibrosis?

Can you let me know is idiopathic pulmonary fibrosis the same as cystic fibrosis?

No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more

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Why does cystic fibrosis be obstructive and idiopathic pulmonary fibrosis restrictive? Smh

Why does cystic fibrosis be obstructive and idiopathic pulmonary fibrosis restrictive? Smh

Cystic fibrosis: Involves large amounts of mucus in the airways. Therefore, it is difficult for air to flow due to mucus obstructing airways.
Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more

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I'd like to know whether stem cell can cure idiopathic pulmonary fibrosis?

I'd like to know whether stem cell can cure idiopathic pulmonary fibrosis?

Not currently: There are no treatments for idiopathic pulmonary fibrosis. Lung transplant results are no great. Numerous drug studies are underway using drugs that slow down or inhilit the fibrotic cascade. ...Read more

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Kindly guide me how to handle idiopathic pulmonary fibrosis, diagnosed in my mom. She is suffering from dry cough now, and feels fatigued while walk.

Help is available: The coalition for pulmonary fibrosis can provide guidance, education and support for families and patients dealing with pulmonary fibrosis. There website is: http://www.Coalitionforpf. Org/

This is a challenging diagnosis--you are not alone. ...Read more

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My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?

My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?

Lung transplant: Other factors are considered too, as age, general health, other chronic diseases, the original lung disease and whether it can recur in the transplanted lung, your father needs to be evaluated in a tertiary care hospital, either a university or a teaching hospital, better if they have a transplant program, wish you and your father wellness ...Read more

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Can pulmonary fibrosis affect young children?

Unusual : Rarely in presence of connective tissue disorders, after certain medications, after chest radiation. ...Read more

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Are there any foods I can eat to heal my pulmonary fibrosis?

It's chronic disease: Pulmonary fibrosis is a chronic disease. It could be idiopatic, or as a result of other diseases like scleroderma, lupus....
No diet can heal your disease but if you have co2 retention than food low in carbohydrates will help with lowering of your carbon dioxide. ...Read more

Dr. Aaron Milstone
628 doctors shared insights

Pulmonary Fibrosis (Definition)

A lung condition in which there is progressive scarring of the lung tissue. Symptoms include shortness of breath, chest pain, fatigue, ...Read more


Dr. Ibrahim Faruqi
173 doctors shared insights

Idiopathic Pulmonary Fibrosis (Definition)

Idiopathic pulmonary fibrosis is a condition of scarring of the lungs with no known cause resulting in worsening cough ...Read more