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Doctor insights on: How Does Cystic Fibrosis Affect The Integumentary System

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Can somebody tell me how can the endocrine system relate to cystic fibrosis?

Can somebody tell me how can the endocrine system relate to cystic fibrosis?

Cystic Fibrosis: The endocrine system is potentially one of the systems involved in cystic fibrosis. There are many different presentations of cf. If the pancreas is affected then supplements may be needed to help digest food. In addition, some CF patients have a form of diabetes. The cff is a good resource for information. Cff. Org
prmg will review your CF records at 858 259 9689 at no cost to you. ...Read more

Dr. William Walsh
992 Doctors shared insights

Cystic Fibrosis (Definition)

A genetic disorder of the lungs and digestive tract. It causes recurrent lung infections and inhibits growth in patients and average life expectancy of patients with cystic fibrosis ...Read more


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What is done to improve the immune system of a cystic fibrosis patient?

What is done to improve the immune system of a cystic fibrosis patient?

Cystic fibrosis: CF is a genetic defect and at this time, it cannot be repaired. Companies such as sangamo pharmaceuticals are working on cures for mono-genetic diseases, and maybe someday a cure could become available. ...Read more

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What does cystic fibrosis do to the pulmonary system on a cellular level?

Mucus & infection: The cells lining the airways don't put out enough water into the airway to make airway secretions thin enough to be coughed out. The mucus that collects clog the airways and let germs grow and thrive instead of being killed. Long-term infection damages the airways and substance of the lung. The airways and lung units gradually fill up with pus and germs and can't take in oxygen or get rid of co2. ...Read more

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Can cystic fibrosis affect both respiratory and digestive system?

Absolutely: The thicker mucous secretions inherent to cystic fibrosis (CF) can cause a relative obstruction in clearing the airway tree of particulate matter/germs. Similarly, these secretions can obstruct the passage of pancreatic enzymes into the intestine leading to mal-digestion. ...Read more

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How does cystic fibrosis affect social development?

How does cystic fibrosis affect social development?

Significantly: CF is associated with repeated lung infections that result in absence from school and social activities. ...Read more

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How does cystic fibrosis affect the patient and their family?

Many ways: This is a chronic disease that can cause a variety of consequences to the patient and their family. This is a very complicated question to be answered briefly here. ...Read more

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How does Cystic Fibrosis affect social development of an individual?

How does Cystic Fibrosis affect social development of an individual?

Chronic illness: There are many components of a chronic disease that are hard to navigate in adolescence. At a time when absolute uniformity is desired, there are medications to take at specific times, there are doctor visits ("Where were you? "), and there are hospitalizations which entirely disrupt social structures. Concerns about infection can also limit social activities. Encourage social interactions. ...Read more

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Does cystic fibrosis affect your physical appearance?

Does cystic fibrosis affect your physical appearance?

Not specifically: Most CF patients that are monitored and receiving regular healthcare can not be picked out in a crowd of people of similar age. If their disease were to go unrecognized and or untreated they would appear ill. ...Read more

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How does cystic fibrosis affect my alveoli and blood capillaries?

How does cystic fibrosis affect my alveoli and blood capillaries?

CF: Cystic Fibrosis (CF) is an inherited disease that causes thick, sticky mucus to form in the lungs, pancreas and other organs. In the lungs, this mucus blocks the airways-even getting down to the small alveoli, causing lung damage and making it hard to breathe. Recent studies show there may be some blood vessel dysfunction causing an impaired exercise tolerance as well. Hope this helps. ...Read more

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Can someone be diagnose with cystic fibrosis in their 40's?

Can someone be diagnose with cystic fibrosis in their 40's?

As a carrier: Genetic carrier testing:
more than 10 million americans are symptomless carriers of the defective CF gene. This blood test can help detect carriers, who could pass CF onto their children. To have cystic fibrosis, a child must inherit one copy of the defective CF gene from each parent. ...Read more

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Why can't cystic fibrosis patient be near each other?

Increased infection: I am not a pulmonary or infectious specialist so I would defer the definitive answer to those specialty physicians. My understanding is that cystic fibrosis patients have increased risk of pulmonary infection. Placing two individuals with the same increased risk together would increase their risk even more. ...Read more

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Why can't cystic fibrosis patients be near each other?

Why can't cystic fibrosis patients be near each other?

Sharing: Patients with cystic fibrosis are highly susceptible to lung infections. As a result, if they spend a lot of time together, they can readily swap infections. This is one case where you should shun your parents' otherwise good advice on sharing. ...Read more

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If I have cystic fibrosis, what happens if I don't take my enzymes?

If I have cystic fibrosis, what happens if I don't take my enzymes?

Stinky, runny poo: No enzymes= poor or no absorption of food products. Poor absorption = bulky stinky stool that are partially digested by the germs in your gut, and significant weight loss for you as your body begins to self destruct. ...Read more

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I'm 10 weeks preg. My dr said I'm a carrier of cystic fibrosis I don't understand?

I'm 10 weeks preg. My dr said I'm a carrier of cystic fibrosis I don't understand?

Pretty common: Various studies cite about 1/40 normal individuals are carries of one CF gene. They have no illness, and will not have a CF child unless their spouse is also a carrier. With 2 carriers 1/4 risk of CF per pregnancy would be possible. Carrier detection studies are often offered to someone who has a cf patient in their family. ...Read more

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How can cystic fibrosis affect p.I.E.S development?

Certainly: Cystic Fibrosis (CF) most common life-limiting genetic disorder of Caucasians, affecting approximately 30K people in the US. A, impacting mainly respiratory function. In recent years patients symptoms better controlled by genetic findings and better medications. Emotional & phys. Development depend on severity, time in hospital, complications. Morb. & mort. Factors afect emotional, cognitive behavior. ...Read more

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I have symptoms of cystic fibrosis. Is it possible to start show the symptoms in my 30's?

Yes: Yes it is possible. Presentation of cystic fibrosis varies greatly, and it is possible, depending on your specific mutation (and other factors) to present at a later age. In order to prevent late diagnoses, all states now have a newborn screen in place for cystic fibrosis. ...Read more

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I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

I have family members with cystic fibrosis. Is it possible to start show the symptoms in my 20's?

Yes: However, usually an adult who is diagnosed so late has usually had chronic problems with cough and "pneumonias". That said I've diagnosed a new case in a 38 year old woman. ...Read more

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What are the chances of a child getting cystic fibrosis among the different racial groups in the u.S.?

Overall 1/3700: Acording to the CF foundation: the overall birth prevalence is 1/3700. It can occur in any race, however the greatest incidence is in caucasians of northern european descent, being 1/2500. The other major groups affected are hispanics 1/13500, african americans 1/15000.
More than 10 million of us carry one part of the defective gene, but to have the disease you must have a copy from both parents. ...Read more

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Could a 49 year old develop cystic fibrosis?

Yes and No: Patients are born with cystic fibrosis. However it can take many years for the disease to become apparent in some patients. Thus, it is possible to be diagnosed with CF later in life but not to develop CF later in life. ...Read more

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L am 58 can I get cystic fibrosis at that age.

L am 58 can I get cystic fibrosis at that age.

No: You are born with cystic fibrosis, you don't "get" it later in life. It may not be diagnosed right away depending on the type and severity of symptoms. For example, a newborn with an intestinal blockage would be picked up quickly, but an older child or even an adult who presented with mostly sinus symptoms might not get diagnosed until later. ...Read more

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What is done for a child with cystic fibrosis?

What is done for a child with cystic fibrosis?

Supportive care: CF patients benefit from active coordinated care involving their pcp and a regional cystic fibrosis care center. These are usually part of a children's hospital and involve pediatric pulmonologists and other respiratory care specialists. ...Read more

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What does it mean if I am a carrier cystic fibrosis?

One gene bad: The cftr gene codes for (has information for your body about) a sodium-chloride transporter on your cell membranes. If you have two bad copies you have cf, if you have one, you are a carrier. As many as 1 in 25 caucasian adults in the us has this mutation. If you are planning on having children, talk to your spouse about genetic counseling, unless your spouse is of Asian or african descent. ...Read more

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What are the common symptoms of having cystic fibrosis?

What are the common symptoms of having cystic fibrosis?

Cough + sputum: If above applies, kiss him/her on the skin. If you taste salt it might be cf. A simple sweat test will rule it in or out. ...Read more

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Might it be that a 49 year old develop cystic fibrosis?

Might it be that a 49 year old develop cystic fibrosis?

Unlikely: At age 49, a diagnosis of cystic fibrosis would be very unlikely. That being said, a diagnosis of pulmonary fibrosis, which is different from cf, could be possible, and generally occurs later in life. Pulmonary fibrosis can give the same signs and symptoms as cf. You can experience shortness of breath, cough, fatigue, and weight loss. Smoking is a risk factor. ...Read more

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How typical are false positives on cystic fibrosis tests?

Not Typical: Certain rare conditions can also lead to high sweat chloride levels (the gold standard test for cystic fibrosis). However, these rare conditions (there's a list) will cause the patient to exhibit different symptoms than those consistent with cystic fibrosis, so the sweat chloride test is considered to be reliable in diagnosing CF in conjunction with the patient's history and physical exam. ...Read more

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Is there a common age to start showing signs of cystic fibrosis?

Birth to teen years: The most common variant of CF is detected at birth or would appear shortly thereafter anyway. Most cases are caught by the teen years, but rarer forms show up as late as 30 or so. ...Read more

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What physical activities are ok for someone with cystic fibrosis?

What physical activities are ok for someone with cystic fibrosis?

Anything: Most individuals with cystic fibrosis can participate in all physicial activities. Salt supplementation is needed because of excess salt loss in CF sweat. Individuals with severe lung disease should discuss what level of activity is safe/appropriate for them with their physician. ...Read more

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What are the chances of having a second child with cystic fibrosis?

1 in 4 or 25%: Genetic counseling prior to pregnancy is very important if there is a family history of cystic fibrosis. There are many options available to parents who have already had a child with cystic fibrosis. ...Read more

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What can cause cystic fibrosis and what are its effects on the body?

Genetic: It's a genetic disease and it has numerous effects on various parts of the body, mainly the respiratory system and the gastrointestinal system.
http://www. Cff. Org/AboutCF/ ...Read more

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Why cystic fibrosis only affects the caucasian population and how the disease may have originated?

Why cystic fibrosis only affects the caucasian population and how the disease may have originated?

Not true: Cystic fibrosis is a metabolic disorder more common in caucasions by present in many populations. The incidence is 1/3500 caucasion, 1/17, 000 african american, 1/80, 000 native american. It arises in mutations in the cftr gene that regulates cellular transport of chloride. There are in excess of 700 known mutations recorded but most common is the delta 508. ...Read more

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Is cystic fibrosis because of mucus?

Kind of...: Cystic fibrosis (CF) is a genetic disease. Patients with the disease are born with a defective gene that is part of the body's system for making mucus, sweat, and digestive fluids. Their mucus is therefore abnormally thick and causes blockages in the lungs, pancreas and other organs that damage them and make them prone to infections and other problems. ...Read more

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Are cystic fibrosis and diabetes related?

In a way: Most patients with diabetes have either a failure of the pancrease (pancrelipase) to produce Insulin or develop resistance to Insulin for various reasons. In cf, there is pancreatic insufficiency due to injury to the pancrease (pancrelipase) from the disease itself... And this can lead to CF related diabetes (where more Insulin is needed). ...Read more

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Atypical cystic fibrosis life expectancy?

Depends: Without a full exam and review of medical records and history of infections secondary to CF would be remiss in trying to become an actuarial. Go see a pulmonologist and discuss the options and likely outcomes. ...Read more