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Doctor insights on: Hereditary Fructose Intolerance

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How many people die from "hereditary fructose intolerance" per year?

How many people die from "hereditary fructose intolerance" per year?

Few: This is easily managed once the diagnosis is made, and a decent pediatrician would spot it by the child becoming sick when fructose is introduced to the diet. In a death (and these are very rare), the pathologist would recognize a metabolic problem and perhaps be able to make the call after the fact; some may be missed so no one can tell you exactly. ...Read more

Fructose (Definition)

Fructose, or fruit sugar, is a simple monosaccharide found in many plants (fruits, vegetables, sugar cane and honey). Fructose is absorbed directly into the bloodstream during digestion. Since 1970 high fructose corn syrup has been increasingly used in the food industry. Excess fructose consumption has been linked to Insulin resistance, obesity, metabolic ...Read more


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Could hereditary fructose intolerance be left undiagnosed until adulthood?

Could hereditary fructose intolerance be left undiagnosed until adulthood?

Yes: Some forms of the disorder may not manifest until adulthood. "Froesch et al. (1963) described 2 adults, aged 33 and 39 years, with fructose intolerance. In addition to the aversion to fructose-containing foods, both had a remarkable absence of dental caries. Swales and Smith (1966) described an affected 21-year-old man, and Kohlin and Melin (1968) reported adult cases." See http://www.omim.org/ ...Read more

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If I had hereditary fructose intolerance how much fructose would I need to consume to cause sudden hypoglycemia. Would a very small amount cause sympt?

Rare: If you are 35 and carry this diagnosis I would only guess that you probably can tolerate small amounts of natural fructose and you should know that amount by now. If this is only a possibility would recommend abstaining from concentrated sugar foods, given your history of hypoglycemia. Talk to your doctor before challenging yourself with large amounts of sugar containing products. ...Read more

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What is fructose intolerance?

Lack digestive Enzm: There are people that do not have the enzyme needed for them to digest and utilize the sugar of most fruits. Without the enzyme, gut bacteria thrive on the sugar and produce gas.The process also draws water through the gut, giving the person cramping, gas and loose stools.The primary way to avoid symptoms is to avoid the fructose. ...Read more

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How can I tell if I have fructose intolerance?

How can I tell if I have fructose intolerance?

Symptoms/test.: This has symptoms like bloating, diarrhea and/or constipation, flatulence, and stomach pain. This has a diagnostic test called a hydrogen breath test and is the current test used for a clinical diagnosis. Fructose is given and, if not absorbes, is metabolized by bacteria that gives off hydrogen and methane. This is detected and anything higher than 12-15ppm is positive, typically 20ppm. ...Read more

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I am fructose intolerance-- is glucrose ok?

I am fructose intolerance-- is glucrose ok?

Not really/fructose.: It depends on when/what type of fructose intolerance you have. If it's malabsorption, you can likely have some fructose, or sweet foods/fruits with a low relative fructose level. If it is hereditary, you likely can't have it at all. Looking at your age, you likely have malabsorption, which means you can have foods with more glucose than fructose, like potatoes, and avoid apples and pears, etc. ...Read more

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Can i not eat fruit if I have a fructose intolerance?

Can i not eat fruit if I have a fructose intolerance?

Many: You can still eat fruit. You just have to limit how much fruit you eat. And specifically you should limit fruits high in fructose (apples, pears, mango, watermelon). Only you will know what your "limit" is, and most people learn through trial and error. ...Read more

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Diagnosed with fructose intolerance. Does this mean I can't eat sugar?

Diagnosed with fructose intolerance. Does this mean I can't eat sugar?

Not really/fructose.: It depends on when/what type of fructose intolerance you have. If it's malabsorption, you can likely have some fructose, or sweet foods/fruits with a low relative fructose level. If it is hereditary, you likely can't have it at all. Looking at your age, you likely have malabsorption, which means you can have foods with more glucose than fructose, like potatoes, and avoid apples and pears, etc. ...Read more