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Doctor insights on: End Stage Idiopathic Pulmonary Fibrosis

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How often should I use oxygen if I have idiopathic pulmonary fibrosis?

How often should I use oxygen if I have idiopathic pulmonary fibrosis?

24hr a day: If you need oxygen, your doctor will let you know, usually round the clock. Best is to get a device that measures oxygen level called oximeter, and keep oxygen saturation above 88%. ...Read more

Idiopathic (Definition)

An idiopathic medical condition is one of unknown or obscure cause. In some conditions, there may be known causes as well. For example, themajority of glaucoma cases are idiopathic (unknown cause), but there are some cases related to eye ...Read more


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How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.

How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.

Sorry: Sorry to hear that. It is a very bad disease with loss of lung function. Being what ultimately causes someone in that situation to die. (transplant?).

Not able to keep the oxygen up, or accumulation of fluid behind the lungs, or a cold/upper respiratory infection, or not being able to breathe out the bad air. With all but the last, not being able to breathe is the bad sign.
...Read more

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What is idiopathic pulmonary fibrosis?

What is idiopathic pulmonary fibrosis?

Lung condition: Ipf is a dangerous condition where scar tissue replaces normal lung tissue choking off normal air units and causing breathlessness. It is a progressive disease with no effective treatment at present. ...Read more

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Can idiopathic pulmonary fibrosis be treated?

Can idiopathic pulmonary fibrosis be treated?

Pirfenidone: Not approve in the us, yet

approved in europe and japan

but not very powerful, unfortunately. ...Read more

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What are the tests for idiopathic pulmonary fibrosis?

What are the tests for idiopathic pulmonary fibrosis?

CT or biopsy: The "gold standard" test for idiopathic pulmonary fibrosis is a lung biopsy, usually via lung surgery. But, nowadays, ct scan has gotten very good at diagnosing ipf, and sometimes this is enough. But, usually, lung biopsy is required to make a diagnosis. ...Read more

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What are the symptoms of idiopathic pulmonary fibrosis?

Shortness of breath: Slowly progressive shortness of breath, chest discomfort, cough with exercise, declining exercise capacity. At advanced stages weight loss leg swelling frank chest pain simulating angina. ...Read more

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Is it true that idiopathic pulmonary fibrosis hereditary?

Is it true that idiopathic pulmonary fibrosis hereditary?

Some forms are: A few rare forms of ipf have been identified and defective genes identified, but this is not the case for th majority of ipf sufferers. There may be a heritable genes for the disease, but they have not been identified. ...Read more

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What does it mean when idiopathic pulmonary fibrosis found?

What does it mean when idiopathic pulmonary fibrosis found?

Scarring...: Idiopathic pulmonary fibrosis means that there is scarring of the lungs and the underlying reason for the scarring is not known. It is typically a slowly progressive disease, typically over years. At the final stages, consideration of a lung transplant can be made so avoid smoking to insure that you would be a candidate, if it progresses to that stage. ...Read more

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Is it rare to suffer from idiopathic pulmonary fibrosis (ipf)?

Is it rare to suffer from idiopathic pulmonary fibrosis (ipf)?

Yes: Ipf is a relatively rare disorder, particularly if the diagnosis has been confirmed. There is a lot of support online, including the pulmonary fibrosis foundation. Look it up! ...Read more

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What are the end life symptoms of idiopathic pulmonary fibrosis?

What are the end life symptoms of idiopathic pulmonary fibrosis?

Shortness of breath: Progressive shortness of breath and inability to sustain normal o2 levels are common end of life symptoms. Sometimes the right side of the heart fails causing lots of leg swelling and fatigue. ...Read more

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Are there any ways to suppress/treat idiopathic pulmonary fibrosis?

Not yet: Unfortunately, no effective treatment for ipf is known. Currently, using n-acetyl- cysteine and possibly an experimental drug called perfenidone may be of benefit; they are not cures or even effective at reversing or arresting progression of disease. ...Read more

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Would being exposed to extreme temperatures affect someone with (idiopathic) pulmonary fibrosis?

Shortness of breath: Temperature extremes are harmful because pulmonary fibrosis prevents adapting to the increased metabolic needs that occur with either cold or hot temperatures. Increased dyspnea (shortness of breath) is the typical consequence. The heart can also be strained because it is under more strain in pulmonary fibrosis. ...Read more

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What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?

What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?

Possible: Some people with ipf can get affected by the cold weather. It really depends on the individual. Usually, during the cold weather, the increase in respiratory viruses (especially flu) can cause trouble in patients with any sort of lung disease. But, it really depends on the individual. ...Read more

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Could being exposed to extreme temperatures have any effect on someone with (idiopathic) pulmonary fibrosis?

In general no.: Exposure to extremes of temperatures is unlikely to have an effect on ipf per se. Though other physiological effects of extremes of temperature can compound the sense of shortness of breath. ...Read more

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Are idiopathic pulmonary fibrosis cystic fibrosis the same?

No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more

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My uncle has idiopathic pulmonary fibrosis, please suggest treatment?

My uncle has idiopathic pulmonary fibrosis, please suggest treatment?

There aren't many...: Unfortunately, there are not many treatments for idiopathic pulmonary fibrosis that have been shown to work. Mainly, the focus is on comfort and symptom management.

Sometimes, oxygen can be of benefit. I would also get him evaluated for pulmonary rehab. Although there is no cure, there are many people who can live a long time with ipf. It depends on how bad it is. He should def. See a lung doc. ...Read more

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Please help, how much or how often should I use oxygen if I have idiopathic pulmonary fibrosis?

Please help, how much or how often should I use oxygen if I have idiopathic pulmonary fibrosis?

Depends on level: If your oxygen level, on room air, is over 90% at rest and with walking, you won't need oxygen. In fact, you won't even qualify for oxygen therapy at home until your level goes down to 88%. Thus, simply having that diagnosis of ipf doesn't necessarily mean you will need oxygen. Now, many people with ipf do need oxygen, but it doesn't necessarily need so. ...Read more

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What is the prognosis for idiopathic pulmonary fibrosis in a 66 year old male?

What is the prognosis for idiopathic pulmonary fibrosis in a 66 year old male?

Depends: The average life expectancy is 3 to 5 years however there are many factors that could change that. For example what stage you are in now. Other diseases you may have, diet, and smoking are a few of the factors that contribute to ur prognosis. There are 2 pulmonary fibrosis meds, Ofev and Esbriet that may help you. Pulmonary rehaTalk with ur lung doctor and see where you stand. Good luck ...Read more

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Are there any treatments to cure idiopathic pulmonary fibrosis?

Unfortunately no.: Unfortunately, there is no real cure. There are still attempts to treat symptoms with bronchodilators, and we will give steroids a try, but overall immunosuppressants don't work. If it gets bad enough, transplant is sometimes an option. ...Read more

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What is the treatment for idiopathic pulmonary fibrosis?

What is the treatment for idiopathic pulmonary fibrosis?

No good treatemtns: Unfortunately, there are no good, effective treatments for idiopathic pulmonary fibrosis. Many have been tried, such as steroids, anti-inflammatory drugs, and a drug called mucomyst, (acetylcysteine) but the studies done have not shown significant efficacy.

Treatment is mainly supportive. ...Read more

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What is the treatment for idiopathic pulmonary fibrosis?

None effective: Unfortunately there are no effective treatments for ipf. Currently n-acetyl cysteine and perfenidone are being studied, but at this time no effective treatment has been found. ...Read more

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Can you let me know is idiopathic pulmonary fibrosis the same as cystic fibrosis?

Can you let me know is idiopathic pulmonary fibrosis the same as cystic fibrosis?

No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more

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Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? Smh

Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? Smh

Cystic fibrosis: Involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways.
Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more

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I'd like to know whether stem cell can cure idiopathic pulmonary fibrosis?

I'd like to know whether stem cell can cure idiopathic pulmonary fibrosis?

Not currently: There are no treatments for idiopathic pulmonary fibrosis. Lung transplant results are no great. Numerous drug studies are underway using drugs that slow down or inhilit the fibrotic cascade. ...Read more

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Kindly guide me how to handle idiopathic pulmonary fibrosis, diagnosed in my mom. She is suffering from dry cough now, and feels fatigued while walk.

Help is available: The coalition for pulmonary fibrosis can provide guidance, education and support for families and patients dealing with pulmonary fibrosis. There website is: http://www. Coalitionforpf. Org/

this is a challenging diagnosis--you are not alone. ...Read more

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My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?

My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?

Lung transplant: Other factors are considered too, as age, general health, other chronic diseases, the original lung disease and whether it can recur in the transplanted lung, your father needs to be evaluated in a tertiary care hospital, either a university or a teaching hospital, better if they have a transplant program, wish you and your father wellness ...Read more

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Is pulmonary fibrosis caused by chemotherapy reversible once the chemotherapy has stopped?

Depends on the fibro: If chemotherapy has resulted in end-stage fibrosis then it is unlikely that the fibrosis can be reversed. There are various ild's that are labelled "pulmonary fibrosis" caused by chemotherapy that are reversible though. ...Read more

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Is pulmonary fibrosis terminal?

Not good news: Pulmonary fibrosis means that the patient has developed abnormal tissue formation (fibrosis) that affects the thin membranes separating the air sacs from the blood vessels making it harder for oxygen to cross from air to the red bleed cells. This disease usually irreversible; it is critical to have an early diagnosis and be managed at an institution and by medical staff familiar with it. ...Read more

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What is "end stage" of pulmonary fibrosis?

Advance lung damage: End stage pulmonary fibrosis is a common term that we use when we do not feel that our medications can reverse or improve the lung damage caused by the lung fibrosis. At that point, we consider the patient for lung transplantation. ...Read more

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What about survival in end stage of pulmonary fibrosis?

Variable: Unfortunately, as a medical term, pulmonary fibrosis means different things to different doctors. Your doctor is in the best position to explain the situation and the likelihood of survival. ...Read more

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How fast can I make my pulmonary fibrosis go away?

How fast can I make my pulmonary fibrosis go away?

You can't.: Pulmonary fibrosis means scar tissue has been deposited in the lungs and this cannot be removed or repaired. Currently there is no effective treatment for the most common forms of pulmonary fibrosis. Lung that is injured can sometimes repair back to normal without fibrosis and some medications are being studied that may have benefit. ...Read more

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Sure, I've heard of pulmonary fibrosis. But now that my child may have it, I want to know what it really does to the body.?

Depends: On the cause of the fibrosis; may processes causes lung scarring (fibrosis). Some are well understood (e.g. Asbestos) and others are under investigation but not yet clearly understood (ipf/uip or so called idiopathic pulmonary fibrosis). Each cause of fibrosis has a different outcome, and some have treatments while others do not (other than transplant). ...Read more

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What can I do to prevent pulmonary fibrosis?

What can I do to prevent pulmonary fibrosis?

NO SMOKING: Avoiding tobacco, avoiding toxic lung injury exposures including certain occupations. Also regular exercise and diet. Unfortunately the most common cause of pulmonary fibrosis is idiopathic or familial about which you can do very little. ...Read more

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Does coughing often mean I could have pulmonary fibrosis?

Does coughing often mean I could have pulmonary fibrosis?

No: Doctors have a saying, "if you are standing on a plain in colorado and you hear hoof beats, don't turn around expecting to see zebras." there are so many other conditions which are more common that I would suspect to cause a cough. Infections like colds and bronchitis when coughing for a week to a month. Asthma or chronic bronchitis when months to years. Others can be found with xrays etc. ...Read more

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Are there any anti-depressants I can use if I have pulmonary fibrosis?

Pulmonary fibrosis: To my knowledge, antidepressants have not been shown to assist with any respiratory aspects of pulmonary fibrosis. It is common for fibrosis patients to be depressed, and may be reasonable that these depressed patients could benefit from antidepressants. ...Read more

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I had T.B which caused pulmonary fibrosis in my upper left lungs. Will it have future implications?

I had T.B which caused pulmonary fibrosis in my upper left lungs. Will it have future implications?

Depends: That depends on the severity of the scarring and the severity depends on how long the TB was present before it was treated. Ask your doctor how bad it is and ask for pulmonary function testing if more than mild. ...Read more

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Newly diagnosed pulmonary fibrosis in 70 year old female with no other medical conditions. What should I do?

See Pulmonologist: Any patient diagnosed with pulmonary fibrosis should be seen by a pulmonologist who can confirm the diagnosis, follow their course and offer appropriate treatments. ...Read more

Dr. Aaron Milstone
627 Doctors shared insights

Pulmonary Fibrosis (Definition)

A lung condition in which there is progressive scarring of the lung tissue. Symptoms include shortness of breath, chest pain, fatigue, ...Read more


Dr. Ibrahim Faruqi
173 Doctors shared insights

Idiopathic Pulmonary Fibrosis (Definition)

Idiopathic pulmonary fibrosis is a condition of scarring of the lungs with no known cause resulting in worsening cough ...Read more