Doctor insights on:
End Stage Idiopathic Pulmonary Fibrosis
How will I know that my mum has only a few weeks/ days before she dies? She's 64yrs old and is in late stages of idiopathic pulmonary fibrosis.
Sorry to hear that. It is a very bad disease with loss of lung function. Being what ultimately causes someone in that situation to die. (transplant?).
Not able to keep the oxygen up, or accumulation of fluid behind the lungs, or a cold/upper respiratory infection, or not being able to breathe out the bad air. With all but the last, not being able to breathe is the bad sign.
Discuss with: Your doctor. Impossible to know with limited info. ...Read more
Lung condition: Ipf is a dangerous condition where scar tissue replaces normal lung tissue choking off normal air units and causing breathlessness. It is a progressive disease with no effective treatment at present. ...Read more
Some forms are: A few rare forms of ipf have been identified and defective genes identified, but this is not the case for th majority of ipf sufferers. There may be a heritable genes for the disease, but they have not been identified. ...Read more
Scarring...: Idiopathic pulmonary fibrosis means that there is scarring of the lungs and the underlying reason for the scarring is not known. It is typically a slowly progressive disease, typically over years. At the final stages, consideration of a lung transplant can be made so avoid smoking to insure that you would be a candidate, if it progresses to that stage. ...Read more
Yes: Ipf is a relatively rare disorder, particularly if the diagnosis has been confirmed. There is a lot of support online, including the pulmonary fibrosis foundation. Look it up! ...Read more
Not yet: Unfortunately, no effective treatment for ipf is known. Currently, using n-acetyl- cysteine and possibly an experimental drug called perfenidone may be of benefit; they are not cures or even effective at reversing or arresting progression of disease. ...Read more
http://www. Nhlbi. Nih. Gov/health/health-topics/topics/ipf/
Shortness of breath: Temperature extremes are harmful because pulmonary fibrosis prevents adapting to the increased metabolic needs that occur with either cold or hot temperatures. Increased dyspnea (shortness of breath) is the typical consequence. The heart can also be strained because it is under more strain in pulmonary fibrosis. ...Read more
What would being exposed to extreme temperaturesdo to someone with (idiopathic) pulmonary fibrosis?
Possible: Some people with ipf can get affected by the cold weather. It really depends on the individual. Usually, during the cold weather, the increase in respiratory viruses (especially flu) can cause trouble in patients with any sort of lung disease. But, it really depends on the individual. ...Read more
No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more
There aren't many...:
Unfortunately, there are not many treatments for idiopathic pulmonary fibrosis that have been shown to work. Mainly, the focus is on comfort and symptom management.
Sometimes, oxygen can be of benefit. I would also get him evaluated for pulmonary rehab. Although there is no cure, there are many people who can live a long time with ipf. It depends on how bad it is. He should def. See a lung doc. ...Read more
Depends on level: If your oxygen level, on room air, is over 90% at rest and with walking, you won't need oxygen. In fact, you won't even qualify for oxygen therapy at home until your level goes down to 88%. Thus, simply having that diagnosis of ipf doesn't necessarily mean you will need oxygen. Now, many people with ipf do need oxygen, but it doesn't necessarily need so. ...Read more
Depends: The average life expectancy is 3 to 5 years however there are many factors that could change that. For example what stage you are in now. Other diseases you may have, diet, and smoking are a few of the factors that contribute to ur prognosis. There are 2 pulmonary fibrosis meds, Ofev and Esbriet that may help you. Pulmonary rehaTalk with ur lung doctor and see where you stand. Good luck ...Read more
No good treatemtns:
Unfortunately, there are no good, effective treatments for idiopathic pulmonary fibrosis. Many have been tried, such as steroids, anti-inflammatory drugs, and a drug called mucomyst, (acetylcysteine) but the studies done have not shown significant efficacy.
Treatment is mainly supportive. ...Read more
None effective: Unfortunately there are no effective treatments for ipf. Currently n-acetyl cysteine and perfenidone are being studied, but at this time no effective treatment has been found. ...Read more
No: Ipf is a disease of older patients that has no known cause and leads to thickening of the soft tissue in the lung. This causes poor movement of oxygen into the bloodstream. CF is a genetic disease usually diagnosed in childhood. Patients have an abnormal protein in some organs that causes mucous to thicken. In the lungs, this results in chronic infections and airway damage. ...Read more
Involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways.
Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more
Kindly guide me how to handle idiopathic pulmonary fibrosis, diagnosed in my mom. She is suffering from dry cough now, and feels fatigued while walk.
Help is available:
The coalition for pulmonary fibrosis can provide guidance, education and support for families and patients dealing with pulmonary fibrosis. There website is: http://www. Coalitionforpf. Org/
this is a challenging diagnosis--you are not alone. ...Read more
My father is diagnosed with idiopathic pulmonary fibrosis, copd, polycythemia and cronic asthmatic bronchitis. Is he a candidate for lung transplant?
Lung transplant: Other factors are considered too, as age, general health, other chronic diseases, the original lung disease and whether it can recur in the transplanted lung, your father needs to be evaluated in a tertiary care hospital, either a university or a teaching hospital, better if they have a transplant program, wish you and your father wellness ...Read more
Not good news: Pulmonary fibrosis means that the patient has developed abnormal tissue formation (fibrosis) that affects the thin membranes separating the air sacs from the blood vessels making it harder for oxygen to cross from air to the red bleed cells. This disease usually irreversible; it is critical to have an early diagnosis and be managed at an institution and by medical staff familiar with it. ...Read more
Advance lung damage: End stage pulmonary fibrosis is a common term that we use when we do not feel that our medications can reverse or improve the lung damage caused by the lung fibrosis. At that point, we consider the patient for lung transplantation. ...Read more
Variable: Unfortunately, as a medical term, pulmonary fibrosis means different things to different doctors. Your doctor is in the best position to explain the situation and the likelihood of survival. ...Read more
You can't.: Pulmonary fibrosis means scar tissue has been deposited in the lungs and this cannot be removed or repaired. Currently there is no effective treatment for the most common forms of pulmonary fibrosis. Lung that is injured can sometimes repair back to normal without fibrosis and some medications are being studied that may have benefit. ...Read more
Sure, I've heard of pulmonary fibrosis. But now that my child may have it, I want to know what it really does to the body.?
Depends: On the cause of the fibrosis; may processes causes lung scarring (fibrosis). Some are well understood (e.g. Asbestos) and others are under investigation but not yet clearly understood (ipf/uip or so called idiopathic pulmonary fibrosis). Each cause of fibrosis has a different outcome, and some have treatments while others do not (other than transplant). ...Read more
No: Doctors have a saying, "if you are standing on a plain in colorado and you hear hoof beats, don't turn around expecting to see zebras." there are so many other conditions which are more common that I would suspect to cause a cough. Infections like colds and bronchitis when coughing for a week to a month. Asthma or chronic bronchitis when months to years. Others can be found with xrays etc. ...Read more
Antihistaminics.: May be antihistaminics without decongestants!Get a more detailed answer ›
I had T.B which caused pulmonary fibrosis in my upper left lungs. Will it have future implications?
Newly diagnosed pulmonary fibrosis in 70 year old female with no other medical conditions. What should I do?
See Pulmonologist: Any patient diagnosed with pulmonary fibrosis should be seen by a pulmonologist who can confirm the diagnosis, follow their course and offer appropriate treatments. ...Read more
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