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Doctor insights on: Cystic Fibrosis Liver

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Are idiopathic pulmonary fibrosis cystic fibrosis the same?

Are idiopathic pulmonary fibrosis cystic fibrosis the same?

No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more

Dr. Mark Pack
2 doctors shared insights

Liver (Definition)

This organ plays a major role in metabolism and has a number of functions in the body, including glycogen storage, decomposition of red blood cells, plasma protein synthesis, hormone production, and detoxification. It lies below the diaphragm in the abdominal-pelvic region of the abdomen. It produces bile, an alkaline compound which aids in digestion via the emulsification of ...Read more


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Atypical cystic fibrosis life expectancy?

Atypical cystic fibrosis life expectancy?

Depends: Without a full exam and review of medical records and history of infections secondary to CF would be remiss in trying to become an actuarial. Go see a pulmonologist and discuss the options and likely outcomes. ...Read more

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What is cystic fibrosis?

Genetic disorder: It is a genetic disorder characterized by abnormal sodium channels, which affect a great deal of problems including the respiratory and digestive systems. It is most commonly diagnosed in infants failing to gain appropriate weight, and in children who have multiple chronic infections. ...Read more

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Is pulmonary fibrosis the same as cystic fibrosis?

Is pulmonary fibrosis the same as cystic fibrosis?

No: Cystic fibrosis is a genetic disease causing abnormal functioning of the mucus glands in the lung and leading to recurrent infections. Pulmonary fibrosis is a disease of progressive scarring causing loss of alveolar units that can have a variety of causes. ...Read more

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What is advanced liver fibrosis?

What is advanced liver fibrosis?

Cirrhosis: Another term will be cirrhosis or replacement of normal tissue by scar tissue. ...Read more

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Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Cystic fibrosis: involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways. Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more

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Can cystic fibrosis cause chronic bronchitis?

Can cystic fibrosis cause chronic bronchitis?

Bronchiectasis: Chronic airway infection in CF is common; it isn't the same as "chronic bronchitis" precisely but has similar traits (copious purulent sputum production, discomfort, airway obstruction). More commonly the chronic infection and mucus plugging lead to airway destruction, dilation in a condition known as bronchiectasis. Google cts of the chest for both and take a look at the differences. ...Read more

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What's parenchymatous liver disease?

What's parenchymatous liver disease?

Liver Disease: The cells of the liver are called the parenchymal cells and make up the bulk of the liver. Therefore, this means that you have disease of the liver cells. Other cells in the liver include the bile duct cells (cholangiocytes), white blood cells (Kupffer cells), and storage cells (stellate cells). ...Read more

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What is chronic liver parenchymal disease with cirrhosis; varices and ascites?

What is chronic liver parenchymal disease with cirrhosis; varices and ascites?

This sounds serious: To translate, you have liver cell damage and scarring (cirrhosis), which caused abnormally elevated portal vein pressures which caused venous distention in esophagus (varices). You also developed fluid in abdominal cavity, because of the high portal vein pressure. This imaging study is showing advanced stage of liver disease. You must get a specialist to treat you. ...Read more

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Is pulmonary fibrosis inherited?

Is pulmonary fibrosis inherited?

Pulmonary fibrosis: While I have not seen it commonly there are some families with a history of pulmonary fibrosis. Most of my office patients and previous fibrosis patients I have come across are the only ones in their family with fibrosis. I have one patient in my practice with several family members with progressive and ultimately fatal fibrosis. She has been evaluated at duke university with a genetic workup. ...Read more

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Cystic fibrosis, is it sexlinked?

Cystic fibrosis, is it sexlinked?

Autosomal recessive.: Cystic fibrosis (CF) is not sex-linked, but autosomal recessive. That means both parents can be silent carriers--totally unaware--then each passes down this recessive (inactive) gene to their child. This child develops CF because both copies of the formerly inactive gene (1 from each parent) now have no genetic "brake" (normal dominant gene) to prevent the CF gene from expressing itself. ...Read more

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Is pulmonary fibrosis genetic?

Is pulmonary fibrosis genetic?

Some are: Some families have multiple members who develop pulmonary fibrosis although sporadic cases are more common. The exact genetic inheritance is unknown. ...Read more

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Is pulmonary fibrosis terminal?

Is pulmonary fibrosis terminal?

Not good news: Pulmonary fibrosis means that the patient has developed abnormal tissue formation (fibrosis) that affects the thin membranes separating the air sacs from the blood vessels making it harder for oxygen to cross from air to the red bleed cells. This disease usually irreversible; it is critical to have an early diagnosis and be managed at an institution and by medical staff familiar with it. ...Read more

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Why is CF called "cystic" and "fibrosis"?

Old Days: Back in the "old days, " patients with CF would frequently die, and the autopsy findings of the lungs showed scarring ("fibrosis") and bubbles ("cysts, " "cystic"). Thus, it was called cystic fibrosis. We know much more now about this disease, but the old name stuck. ...Read more

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Are cystic fibrosis and diabetes related?

In a way: Most patients with diabetes have either a failure of the pancrease (pancrelipase) to produce Insulin or develop resistance to Insulin for various reasons. In cf, there is pancreatic insufficiency due to injury to the pancrease (pancrelipase) from the disease itself... And this can lead to CF related diabetes (where more Insulin is needed). ...Read more

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Conditions that mimic cystic fibrosis?

The list goes on : There are a whole variety of illnesses that can mimic CF from chronic cough , asthma , to immunodeficiency, broncho pulmonary dysphasia celiac disease , Alpha 1-anti trypsin deficiency. ...Read more

Dr. William Walsh
992 doctors shared insights

Cystic Fibrosis (Definition)

A genetic disorder of the lungs and digestive tract. It causes recurrent lung infections and inhibits growth in patients and average life expectancy of patients with cystic fibrosis ...Read more