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Doctor insights on: Cystic Fibrosis And Creon

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Why is CF called "cystic" and "fibrosis"?

Why is CF called "cystic" and "fibrosis"?

Old Days: Back in the "old days, " patients with CF would frequently die, and the autopsy findings of the lungs showed scarring ("fibrosis") and bubbles ("cysts, " "cystic"). Thus, it was called cystic fibrosis. We know much more now about this disease, but the old name stuck. ...Read more

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Dr. William Walsh
998 doctors shared insights

Cystic Fibrosis (Definition)

A genetic disorder of the lungs and digestive tract that causes repeated lung infections and inhibits ...Read more


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Was diagnosed with cystic fibrosis. What is it like living with cystic fibrosis?

Was diagnosed with cystic fibrosis. What is it like living with cystic fibrosis?

It depends: It really depends on the severity of the disease. Not all patients experience the same symptoms and the same course. ...Read more

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Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Cystic fibrosis: involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways. Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more

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What is cystic fibrosis?

Genetic disorder: It is a genetic disorder characterized by abnormal sodium channels, which affect a great deal of problems including the respiratory and digestive systems. It is most commonly diagnosed in infants failing to gain appropriate weight, and in children who have multiple chronic infections. ...Read more

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Are cystic fibrosis and diabetes related?

In a way: Most patients with diabetes have either a failure of the pancrease (pancrelipase) to produce Insulin or develop resistance to Insulin for various reasons. In cf, there is pancreatic insufficiency due to injury to the pancrease (pancrelipase) from the disease itself... And this can lead to CF related diabetes (where more Insulin is needed). ...Read more

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How are meconium and meconium ileus in cystic fibrosis different?

How are meconium and meconium ileus in cystic fibrosis different?

Yes: Meconium is the normal fecal debris composing the accumulated intestinal contents at birth.It is heavily colored by bile, dark and sticky. Meconium ileus can occur when the meconium has abnormal glue like stickiness caused by CF and will not empty from the bowel.The blockage can require emergency surgery. ...Read more

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What is a?Multi cystic pancreas?

What is a?Multi cystic pancreas?

May be IPMN: Multiple cystic lesions in the pancreas may represent a relatively rare condition called ipmn. Imaging can clarify the suspicion of ipmn, but sometimes endoscopy with a sampling of the fluid is necessary. It they represent ipmn, some surveillance program is recommended and depending on the size and pattern of spread within the pancreas, surgery may be warranted. ...Read more

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How much can a lung transplant help with cystic fibrosis?

How much can a lung transplant help with cystic fibrosis?

Can benefit some: Lung transplantation is an option when the medical regimen can not prevent further decline in end stage lung disease. The timing of the transplantation is important in maximizing the benefit of the transplant. The average survival at one year is around 90%, five years is approx 55% depending on the center. I hope that this helps. Prmg pediatrics/respiratory fax 858 259 9689 for ?S. ...Read more

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Can you get a pancreas transplant in cystic fibrosis?

Can you get a pancreas transplant in cystic fibrosis?

Yes: Yes you can. Some patients can get a lung pancreas or a liver, pancreas. They have done very well at our institution. ...Read more

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Can someone have addison's disease and cystic fibrosis?

Can someone have addison's disease and cystic fibrosis?

Yes, they CAN, but: Addison's disease has been associated with other autoimmune glandular disorders, including malabsorption and type i diabetes. But cf, although having pancreatic (including diabetes i) & GI deficiencies (malabsorption), is a chromosomal not autoimmune disorder. Their association would be purely coincidental. See: neufeld, m, et al. Medicine: september 1981 - volume 60 - issue 5 - ppg 355-362. ...Read more

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Why do sufferers of cystic fibrosis have heart and lung transplants?

Why do sufferers of cystic fibrosis have heart and lung transplants?

Usually not: Most people with CF have neither, and almost never have a heart/lung transplant if thy do. Both lungs are usually transplanted partially to reduce the risk of infection. ...Read more

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Can you die of cystic fibrosis?

Yes but: Yes but with early diagnosis and regular care and adherence to prescribed therapy by a pediatric pulmonologist the long term survival has improved greatly in the past two decades. ...Read more

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What are myelodysplasia and pulmonary fibrosis?

What are myelodysplasia and pulmonary fibrosis?

Myelodysplasia...: and myelofibrosis are both diseases of the bone marrow that impair normal red and white blood cell production. Like the leukemias they occur as a result of mutations in bone marrow stem cells that occur during your lifetime. Despite a similar sounding name, pulmonary fibrosis is an unrelated disease resulting in scarred lung tissue and impaired breathing function. ...Read more

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Can cystic fibrosis cause chronic bronchitis?

Can cystic fibrosis cause chronic bronchitis?

Bronchiectasis: Chronic airway infection in CF is common; it isn't the same as "chronic bronchitis" precisely but has similar traits (copious purulent sputum production, discomfort, airway obstruction). More commonly the chronic infection and mucus plugging lead to airway destruction, dilation in a condition known as bronchiectasis. Google cts of the chest for both and take a look at the differences. ...Read more

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Best milk for people with poly cystic kidney disease?

Best milk for people with poly cystic kidney disease?

Potassium issue?: Polycystic kidney disease is a genetic disease that leads to cystic enlargement of the kidneys (often liver as well) accompanied by decreased kidney function and eventually kidney failure. The peak age for kidney failure is the 5-6th decade. I don't see why and adult with PKD could not have milk (cow) with coffee or cereal. Milk is high in potassium--is that the reason? Needs restriction. ...Read more

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Can you die of cystic fibrosis?

Yes but: Yes but with early diagnosis and regular care and adherence to prescribed therapy by a pediatric pulmonologist the long term survival has improved greatly in the past two decades. ...Read more

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Dr. Barry Rosen
57 doctors shared insights

Pancreatin (Definition)

Pancreatin ...Read more


Dr. Tiffanie Noonan
57 doctors shared insights

Creon (Definition)

Creon ...Read more