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Doctor insights on: Congenital Hepatic Fibrosis

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Are idiopathic pulmonary fibrosis cystic fibrosis the same?

Are idiopathic pulmonary fibrosis cystic fibrosis the same?

No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more

Hepatic (Definition)

Hepatic refers to something that is ...Read more


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Is pulmonary fibrosis inherited?

Is pulmonary fibrosis inherited?

Pulmonary fibrosis: While I have not seen it commonly there are some families with a history of pulmonary fibrosis. Most of my office patients and previous fibrosis patients I have come across are the only ones in their family with fibrosis. I have one patient in my practice with several family members with progressive and ultimately fatal fibrosis. She has been evaluated at duke university with a genetic workup. ...Read more

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Is pulmonary fibrosis terminal?

Is pulmonary fibrosis terminal?

Not good news: Pulmonary fibrosis means that the patient has developed abnormal tissue formation (fibrosis) that affects the thin membranes separating the air sacs from the blood vessels making it harder for oxygen to cross from air to the red bleed cells. This disease usually irreversible; it is critical to have an early diagnosis and be managed at an institution and by medical staff familiar with it. ...Read more

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Is pulmonary fibrosis genetic?

Is pulmonary fibrosis genetic?

Some are: Some families have multiple members who develop pulmonary fibrosis although sporadic cases are more common. The exact genetic inheritance is unknown. ...Read more

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Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Why does cystic fibrosis is obstructive and idiopathic pulmonary fibrosis restrictive? smh

Cystic fibrosis: involves large amounts of mucus in the airways. Therefore it is difficult for air to flow due to mucus obstructing airways. Pulmonary fibrosis involves diffuse scar tissue in the lung parenchyma, making it difficult to expand (Restrictive). ...Read more

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Is pulmonary fibrosis the same as cystic fibrosis?

Is pulmonary fibrosis the same as cystic fibrosis?

No: Cystic fibrosis is a genetic disease causing abnormal functioning of the mucus glands in the lung and leading to recurrent infections. Pulmonary fibrosis is a disease of progressive scarring causing loss of alveolar units that can have a variety of causes. ...Read more

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What is chronic liver parenchymal disease with cirrhosis; varices and ascites?

What is chronic liver parenchymal disease with cirrhosis; varices and ascites?

This sounds serious: To translate, you have liver cell damage and scarring (cirrhosis), which caused abnormally elevated portal vein pressures which caused venous distention in esophagus (varices). You also developed fluid in abdominal cavity, because of the high portal vein pressure. This imaging study is showing advanced stage of liver disease. You must get a specialist to treat you. ...Read more

Dr. Ziad Akl Dr. Akl
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Increased /coarse hepatic parenchymal echotexture (liver parenchymal disease ) with prominent portal vein and splenomegaly? Wat it means

Dr. Ziad Akl Dr. Akl
2 doctors agreed:
Increased /coarse hepatic parenchymal echotexture (liver parenchymal disease ) with prominent portal vein and splenomegaly?  Wat it means

Severe damage: When damage to the liver occurs for a long time, meaning years, the liver becomes scarred and the veins that bring blood to the liver become distended because of resistance inside the liver. This increased pressure causes the spleen to take more blood and become enlarged. This is called cirrhosis of the liver and can be due to any number of things including alcohol and viral hepatitis. ...Read more

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Is pulmonary hypertension acquired disease?

Is pulmonary hypertension acquired disease?

Generally yes: Usually, it is acquired; however, up to 5% of patients with pulmonary arterial hypertension (PAH) may have a genetic or heritable cause. ...Read more

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Cure of diffuse renal parenchymal disease?

Kidney: None, all you can do is protect the remaining portion of your kidneys under the care of a nephrologist. ...Read more

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Atypical cystic fibrosis life expectancy?

Atypical cystic fibrosis life expectancy?

Depends: Without a full exam and review of medical records and history of infections secondary to CF would be remiss in trying to become an actuarial. Go see a pulmonologist and discuss the options and likely outcomes. ...Read more

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Can liver problems cause pulmonary fibrosis?

Can liver problems cause pulmonary fibrosis?

No: Cirrhosis is associated with two other lung disorders which can cause similar symptoms to pulmonary fibrosis. These are called hepatopulmonary syndrome and portopulmonary hypertension. These only occur if cirrhosis is present. If it goes on long enough without treatment, portopulmonary hypertension can cause permanent injury to the lung. ...Read more

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Bilateral lung nodules,Atelectasis prior papilloma thyroid CA.Pituitary Adenoma,Chiari Malformation,FMD,enlarged common bile duct no stones. Genetic?

Bilateral lung nodules,Atelectasis prior papilloma thyroid CA.Pituitary Adenoma,Chiari Malformation,FMD,enlarged common bile duct no stones. Genetic?

Maybe genetic: Probably should have genetic consult. Forinstance Chiari malformation, fibromuscular dysplasia, and thyroid cancer can be associated with neurofibromatosis. Lung nodules are non specific and can be from some infections but also metastatic disease sometimes from papillary thyroid cancer. You may want to consult a geneticist physician. ...Read more

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Can echogenicity of hepatic parenchyma is borderline mild mean auto immune hepatitis?

Can echogenicity of hepatic parenchyma is borderline mild mean auto immune hepatitis?

Fatty liver likely: Lots of substances may "infiltrate" the liver & increase echogenicity (sound waves bounce off liver better). Fatty liver is most common--due to diabetes, high cholesterol, obesity, drinking too much alcohol. Lose weight & stop alcohol consumption if these are your problems. Fatty liver with abnormal liver functions (blood tests) is however considerably more concerning than just an echogenic liver. ...Read more

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What is diffuse renal parenchymal disease?

What is diffuse renal parenchymal disease?

Kidney Disease: "diffuse" means all over the kidney, "parenchymal" means the solid part of the kidney that filters the liquid waste products out of the blood, and "disease" means something is wrong. Typically "diffuse parenchymal disease" means an overall medical problem with the kidney, such as diabetic nephropathy, or post-streptococcal nephritis. In the pediatric world we use this term slightly differently. ...Read more

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What genetic syndromes associated with congenital hydronephrosis ?

What genetic syndromes associated with congenital hydronephrosis ?

Genetics : There are many causes of hydronephrosis. Often hydronephrosis is found on prenatal ultrasounds but is not seen on postnatal ultrasounds. Any kidney or bladder malformation can cause hydronephrosis. In infants, posterior urethral valves, kidney stones, cystic kidneys, abdminal masses or any stenosis of the urethra or ureters may cause hydronephrosis. ...Read more

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Liver biopsy = hepatic parenchyma showing moderate to severe chronic hepatitis w/bridging fibrosis &focal changes of early micronodular cirrhosis. Grade 3-4 stage 3-4. Can thyroid cause this? Or what?

Liver biopsy = hepatic parenchyma showing moderate to severe chronic hepatitis w/bridging fibrosis &focal changes of early micronodular cirrhosis. Grade 3-4 stage 3-4. Can thyroid cause this? Or what?

No: thyroid problems do not cause cirrhosis. you may have an autoimmune hepatitis leading to cirrhosis, which could be associated with thyroid disease. There are many causes of cirrhosis, ask your doctor to test you, as most can be checked with a blood test. ...Read more

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Dr. Louis Gallia
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Hepatic Fibrosis (Definition)

There is excessive connective ...Read more