Top
20
Doctor insights on: Billary Atresia

Share
1

1
Biliary atresia treatment?

Biliary atresia treatment?

Kasai procedure: Biliary atresia is most often diagnosed in the neonates. The first line treatment is a surgical procedure called portoenterotomy (kasai) in which a loop of intestine is connected to the liver to act as a conduit for bile drainage in place of the missing bile ducts. The beneficial effects of this procedure, however, is often short-lived many children went on to require liver transplantation. ...Read more

See 1 more doctor answer
Dr. Tiffanie Noonan
1 doctor shared a insight

Biliary (Definition)

Biliary means anything related to the production, storage, secretion, or flow of bile, whether in the liver, bile ducts, gallbladder, ...Read more


2

2
Is biliary atresia hereditary?

No: There is no proof that it is hereditary. Fortunately it is quite rare. ...Read more

See 1 more doctor answer
3

3
Tracheo-oesophageal fistula and oesophageal atresia hereditary?

Tracheo-oesophageal fistula and oesophageal atresia hereditary?

Not usually: Esophageal atresia with or with out fistula is usually sporadic. There area a few cases ( and i mean very few) in the literature where a parent had ea-tef and had a child with same. It is reportable. ...Read more

4

4
How is biliary atresia typically diagnosed?

Multidisciplinary: This diagnosis is made by a team of neonatologists, pediatric surgeons and pediatric gastroenterologists. It includes blood test, an ultrasound, a nuclear scan called hida scan to evaluate drainage of the liver, a liver biopsy and finally a cholangiogram. As you can see it is not straightforward and that is why so many specialists are required. ...Read more

See 3 more doctor answers
5

5
What is the liver biliary atresia?

What is the liver biliary atresia?

Biliary atresia: Biliary atresia is a congenital scarring of the biliary ducts. These ducts transport bile made in the liver to the intestine so one can digest fats. The ducts scar and obliterate. Bile then cannot exit the liver which poisons the liver. These infants need corrective surgery before they are 2 months old. ...Read more

See 1 more doctor answer
6

6
Is biliary atresia detected before birth?

Is biliary atresia detected before birth?

No: Biliary atresia is unsuspected until there is a persistent rise in bilirubin of the direct type. Initial imaging study should be a preprandial gall bladder ultrasound to see if gall bladder is present. ...Read more

See 1 more doctor answer
7

7
Is primary biliary cirrhosis hereditary?

Basically no: There's a pair of genes that carry the ability to develop the disease and these run in families, but it's not inherited like sickle cell, huntington's or some of the other familiar entities. http://www.medicalnewstoday.com/releases/151640.php. ...Read more

8

8
Bilateral lung nodules,Atelectasis prior papilloma thyroid CA.Pituitary Adenoma,Chiari Malformation,FMD,enlarged common bile duct no stones. Genetic?

Bilateral lung nodules,Atelectasis prior papilloma thyroid CA.Pituitary Adenoma,Chiari Malformation,FMD,enlarged common bile duct no stones. Genetic?

Maybe genetic: Probably should have genetic consult. Forinstance Chiari malformation, fibromuscular dysplasia, and thyroid cancer can be associated with neurofibromatosis. Lung nodules are non specific and can be from some infections but also metastatic disease sometimes from papillary thyroid cancer. You may want to consult a geneticist physician. ...Read more

10

10
What is the disorder biliary atresia?

Bile Duct Blockage: The bile duct carries the bile formed in the liver to the small intestine. Any disease that narrows, scars, or obstructs the duct can be called atresia. In some cases a patient is born with a narrow duct, called congenital atresia. In other cases chronic inflammation, infection, or even rejection of a liver transplant can cause scarring or narrowing of the duct. ...Read more

See 2 more doctor answers
11

11
What is treatment painful liver segment 7 subcapsular benign biliary cyst, dilated bile duct? 5cmx5cmx1.3cm. Past history lapchole with bile leak 2005

What is treatment painful liver segment 7 subcapsular benign biliary cyst, dilated bile duct? 5cmx5cmx1.3cm. Past history lapchole with bile leak 2005

Need further testing: even though you have had your gallbladder removed . you still can form stones within the common bile duct. which will cause billiary pain. Have your doctor check your liver function tests---if elevated do an ultrasound of the liver ...Read more

13

13
What is done for biliary atresia?

Depends on situation: If picked up early enough, some respond to surgery to re-establish bile flow. If operated later than 10 weeks of age, most will need a liver transplant to survive. All cases are quite unique & conferring with the treatment team will provide the best information. ...Read more

See 1 more doctor answer
14

14
What syndrome has hypoplastic ventricle, pulmonary and tricuspid atresia?

What syndrome has hypoplastic ventricle, pulmonary and tricuspid atresia?

Variable: Could be a dorv double outlet right ventricle which can incorporate the defects mentioned. ...Read more

15

15
What does diffuse dilatation of common bile duct & mild dilatation of hepatic ducts mean? Maximal luminal (phenobarbital) diam. of common is 14-15mm. MRI sched. Liver

What does diffuse dilatation of common bile duct & mild dilatation of hepatic ducts mean? Maximal luminal (phenobarbital) diam. of common is 14-15mm. MRI sched. Liver

Dilated bile duct: The bile duct is the duct the drains bile out of the river and into the intestines. Dilated bile duct can be a sign of pancreatic, bile duct, liver,or gallbladder disease. It is an important sign, and it definitely needs to be evaluated until a cause is identified and taken care of. Do not hesitate to get the MRI and follow up with your doctor on the results. Good luck. ...Read more

16

16
What exactly is biliary atresia?

What exactly is biliary atresia?

Birth defect: Malformation and scarrng obliteration of the bile ducts. Starts at birrth and progresses. Any infant who is jaundiced after one month of age needs a bilirubim level and a gallbladder ultrasound. Will need surgical correction prior to 60 days of life. ...Read more

See 1 more doctor answer
17

17
How is biliary atresia generally treated?

Surgery: Once the diagnosis is made and if the baby is considered an appropriate candidate, the approach is surgical. As the problem is lack of drainage of bile from the liver to the intestine, a new connection is made between the liver and intestine. It is called a portoenterostomy or a kasai procedure. Sometimes the child is not a candidate and may need transplantation of liver. ...Read more

See 1 more doctor answer
18

18
What causes pancreatic ductal dilation?

What causes pancreatic ductal dilation?

Pancreatic duct dila: This can happen in chronic panceatitis, or if there is a pancreatic neoplasm ( tumor) . Sometimes there are benign tumors in the duct that can eventually become malignant so it is important to check them out. Technically gallstones that are stuck at the spincter of Vater causing pancreatitis can result in pancreatic duct dilatation as can inflammation post ERCP. ...Read more