Top
20
Doctor insights on: Absent Pulmonary Valve

Share
Dr. Jan Lei Iwata
12 doctors shared insights

Absent Pulmonary Valve (Overview)

Absent pulmonary valve is a congenital defect (occurring at birth). The pulmonary valve of the heart is absent or poorly formed. It can occur as a single defect or as the part of a complex congenital heart condition such as Tetralogy of Fallot.


Dr. Jan Lei Iwata
12 doctors shared insights

Absent Pulmonary Valve (Overview)

Absent pulmonary valve is a congenital defect (occurring at birth). The pulmonary valve of the heart is absent or poorly formed. It can occur as a single defect or as the part of a complex congenital heart condition such as Tetralogy of Fallot.


2

2
What are the symptoms of absent pulmonary valve?

What are the symptoms of absent pulmonary valve?

Depends: Pulmonary valve atresia causes intense cyanosis and possibly respiratory distress. An absent pulmonary valve (tetralogy of fallot with absent pulmonary valve syndrome) presents with a heart murmur and respiratory distress. They usually have very dilated pulmonary arteries that compress the airways.

See 1 more doctor answer
3

3
What sort of problem is an absent pulmonary valve?

What sort of problem is an absent pulmonary valve?

Rare CHD: A rare congenital heart defect. The pulmonary valve doesn’t form and not enough blood can flow to the lungs to get oxygen; only through the PDA (patent ductus arteriosus). It often occurs as part of a condition called tetralogy of fallot. There is usually a hole between the left and right ventricles of the heart (ventricular septal defect). Surgery as a newborn is required.

See 1 more doctor answer
4

4
What is the definition or description of: Absent pulmonary valve?

What is the definition or description of: Absent pulmonary valve?

Absent pulmonary: Absent pulmonary valve is a congenital defect (occurring at birth). The pulmonary valve of the heart is absent or poorly formed. It can occur as a single defect or as the part of a complex congenital heart condition such as Tetralogy of Fallot.

5

5
Is anyone born or diagnosed with a v.S.D with absent pulmonary valve?

Is anyone born or diagnosed with a v.S.D with absent pulmonary valve?

Rare defect: Absent pulmonary valve syndrome is a rare congenital heart defect. Some of the features are similar to tetralogy of fallot. An important difference in most babies with absent pulmonary valve syndrome is that the pulmonary arteries are very large, and often associated with problems with the airways. Surgery is required to repair the problems in the heart and repair the pulmonary arteries.

6

6
Where can I find other people with a v.S.D with absent pulmonary valve?

Where can I find other people with a v.S.D with absent pulmonary valve?

ACHD - National Org: I think your best source of both information and the ability to connect with others with VSD/absent pulmonary valve is the American Congenital Heart Disease Association. (www.achaheart.org) website. They will have their annual meeting in Chicago Sept 5th-7th and much of it revolves around patients and their families. I have spoke at it before and it is an excellent meeting. Please check it out.

See 1 more doctor answer
7

7
What happens if you are ?Born?With a v.S.D with absent pulmonary valve?

What happens if you are ?Born?With a v.S.D with absent pulmonary valve?

Respiratory distress: Absent pulmonary valve syndrome is a rare form of congenital heart disease. There are some features that are similar to tetralogy of fallot. Absent pulmonary valve syndrome is different than pulmonary valve atresia. Corrective surgery is required. Typically, the dominant feature early is respiratory distress due to compression of the trachea and bronchi by enlarged pulmonary arteries.

See 2 more doctor answers
8

8
What are the advantages and disadvantages of different treatments for absent pulmonary valve?

What are the advantages and disadvantages of different treatments for absent pulmonary valve?

Probably none needed: If born this way, there probably is nothing that absolutely needs to be done because of an absent pulmonic valve per se. The valve adds to efficient function of the "right" (vs. Left) sided heart chambers, but the heart may compensate by itself. Any active intervention may be fraught with more risk than benefit, but consulting a pediatric cardiologist is prudent to confirm this & get best advice.

See 1 more doctor answer
9

9
Tof corrected 20 years back, now pulmonary valve to be replaced with bovine valve. Is there any other option. Which is the best valve option.

Tof corrected 20 years back, now pulmonary valve to be replaced with bovine valve. Is there any other option.  Which is the best valve option.

Talk to your doctor: This is the role your doctor should be taking- talk to you about the pros and cons on different options. If you don't trust his judgment, then you need to get a second opinion. For example, if you were a muslim, then a pork valve would not be an option for you regardless how good it may be.

10

10
When i was 8yrs old, my pulmonary valve was removed, not replaced, from stenosis. How common is this?

When i was 8yrs old, my pulmonary valve was removed, not replaced, from stenosis. How common is this?

Incidence: This anomaly occurs in about 8 of every 10,000 people (live births).

11

11
How do you get treated if you have pulmonary valve stenosis?

How do you get treated if you have pulmonary valve stenosis?

Depends: Depends on age, size of infundibulum, pulmonary annulus, tricuspid or bicuspid valve or degree of pulmonary atresia, primary or redo after previous congenital cardiac surgical repair. If it is a newborn and the annulus size is good and magoon ratio good, simple balloon angioplasty can be considered. Later on stented bioprosthesis can be considered. Otherwise pulmonary homograft at birth may be need.

12

12
Information/experiences with pulmonary valve replacement risks?

Information/experiences with pulmonary valve replacement risks?

Indication?: Assuming an adult patient, it would be important to determine if replacement is truly necessary. If the valve is very tight and creating right heart failure or low output syndrome (quite rare), valvuloplasty or removal without replacement may suffice. If the valve is infected, other complications may be present. Best left to the attending cardiologist and consulting surgeon.

13

13
I have 38 and have to have pulmonary valve replacement. Is it animal or other?

I have 38 and have to have pulmonary valve replacement. Is it animal or other?

Discuss with MD: You really need to discuss this with your surgeon. It is way too involved of a discussion for this kind of board.

14

14
What are the postoperative recommendations for pulmonary valve stenosis repair in infants?

What are the postoperative recommendations for pulmonary valve stenosis repair in infants?

Normal: Aswer somewhat depends upon how it was fixed - surgically or catheter - as well as the result. But most ps has a very good outcome and patients have a normal life. Post-op care is quite minimal.

15

15
What is the function of the pulmonary valve?

What is the function of the pulmonary valve?

Flow direction: Pulmonic valve like all other heart valves, directs the flow from one chamber to another, in this case from the right ventricle to the lungs. It allows the flow to be organized and the timing of flow to be proper.

See 1 more doctor answer
16

16
What is the definition or description of: pulmonary valve?

Valve in the heart: The heart has 4 chambers. The right ventricle is the pumping chamber whic h pushes blood into the lungs so oxygen can be put into the blood. When the right ventricle squeezes, the pulmonary valve opens and blood flows into the lungs. When the right ventricle relaxes to fill, the pulmonary valve closes so blood can't flow backwards back into the heart.

17

17
Can you explain "Mobile pulmonary Valve with increased flow velocity." ?

Can you explain "Mobile pulmonary Valve with increased flow velocity."  ?

I can try: The pulmonary valve keeps blood from flowing back into your heart as it is pumped out into the lungs. I'm not sure what "mobile" means in this context, though my sense is that's what it should be - freely opening and closing. The increased flow velocity means the blood is moving faster than expected across the valve. If you are having any heart or lung symptoms, I'd see your doctor.

18

18
What is pulmonary valve stenosis?

What is pulmonary valve stenosis?

Pulmonary stenosis: Pulmonary stenosis is used to describe a condition in which the heart valve which is associated with the right-sided heart chamber which pumps deoxygenated blood to the lungs is narrowed thereby impeding blood flow to the lungs.

19

19
How is a pulmonary valve stenosis treated?

How is a pulmonary valve stenosis treated?

Pulmonary stenosis: Treatment for pulmonary valve stenosis varies depending upon the severity of stenosis and symptoms, and whether this is an isolated finding or there are other comorbid issues. Generally patients with mild to moderate stenosis may not require intervention, whereas patients with moderate to severe stenosis might require a catheter -or surgical-based approach to open up the narrowing.

20

20
Can pulmonary valve stenosis cure itself over time?

No: Pulmonary valve stenosis may be mild and remain so for many years, but it does not go away without treatment.

Dr. William Singer
1 doctor shared a insight

Valve (Definition)

A valve is a structure that regulates the direction of flow. The heart is a special kind of pump. It moves blood by squeezing and relaxing. There are 4 chambers and each chamber has a valve. This keeps blood from moving backwards when the heart squeezes. When a chamber squeezes it lets the blood move forward but when the chamber is relaxed it prevents the blood from ...Read more


Pulmonary Valve (Definition)

The heart has 4 chambers. The right ventricle is the pumping chamber whic h pushes blood into the lungs so oxygen can be put into the blood. When the right ventricle squeezes, the pulmonary valve opens and blood flows into the lungs. When the right ventricle relaxes to fill, the pulmonary valve closes so blood can't flow backwards ...Read more