Doctor insights on:
Atypical Cystic Fibrosis
Depends: Without a full exam and review of medical records and history of infections secondary to CF would be remiss in trying to become an actuarial. Go see a pulmonologist and discuss the options and likely outcomes. ...Read more
No: Two completely different diseases. CF is an inherited disorder leading to failure to clear mucus and repeated infections. It does end up with fibrosis in the lungs. Idiopathic fibrosis is a disease of unknown cause where scar tissue replaces normal lung and eventually causes respiratory failure. ...Read more
Genetic disorder: It is a genetic disorder characterized by abnormal sodium channels, which affect a great deal of problems including the respiratory and digestive systems. It is most commonly diagnosed in infants failing to gain appropriate weight, and in children who have multiple chronic infections. ...Read moreSee 1 more doctor answer
Bronchiectasis: Chronic airway infection in CF is common; it isn't the same as "chronic bronchitis" precisely but has similar traits (copious purulent sputum production, discomfort, airway obstruction). More commonly the chronic infection and mucus plugging lead to airway destruction, dilation in a condition known as bronchiectasis. Google cts of the chest for both and take a look at the differences. ...Read moreSee 1 more doctor answer
Cyst formation: Adenomatoid nodule - fibrotic stroma and glands ( adenoma). When adenomatoid nodule exists for a while and compresses blood vessels and surrounding tissue, hemorrhages and necrosis possible, and finally, in this place tissue degeneration with cyst formation. Example, leiomyomas of uterus sometimes reveal cystic degeration. ...Read more
Old Days: Back in the "old days, " patients with CF would frequently die, and the autopsy findings of the lungs showed scarring ("fibrosis") and bubbles ("cysts, " "cystic"). Thus, it was called cystic fibrosis. We know much more now about this disease, but the old name stuck. ...Read moreSee 1 more doctor answer
Pulmonary fibrosis: While I have not seen it commonly there are some families with a history of pulmonary fibrosis. Most of my office patients and previous fibrosis patients I have come across are the only ones in their family with fibrosis. I have one patient in my practice with several family members with progressive and ultimately fatal fibrosis. She has been evaluated at duke university with a genetic workup. ...Read moreSee 1 more doctor answer
Autosomal recessive.: Cystic fibrosis (CF) is not sex-linked, but autosomal recessive. That means both parents can be silent carriers--totally unaware--then each passes down this recessive (inactive) gene to their child. This child develops CF because both copies of the formerly inactive gene (1 from each parent) now have no genetic "brake" (normal dominant gene) to prevent the CF gene from expressing itself. ...Read more
Dads c't scan multiple small clustered nodules centrilobular config worsening. Has bronchectasis. Considerations Atypical mycobacterial infec. Cure?
Very possible. : Needs sampling and specific sensitivities if in fact the infection is the cause. Treatment can last 1-2 years. However, other diagnostic possibilities and u should see a lung specialist to consider biopsied and cultures. Good luck ...Read more
In a way: Most patients with diabetes have either a failure of the pancrease (pancrelipase) to produce Insulin or develop resistance to Insulin for various reasons. In cf, there is pancreatic insufficiency due to injury to the pancrease (pancrelipase) from the disease itself... And this can lead to CF related diabetes (where more Insulin is needed). ...Read moreSee 1 more doctor answer
- Talk to a doctor live online for free
- Atypical cystic fibrosis symptoms
- Atypical cystic fibrosis life expectancy
- Cystic fibrosis
- Ask a doctor a question free online
- Is cyanosis a symptom of cystic fibrosis?
- Is jaundice a symptom of cystic fibrosis?
- Prenatal test for cystic fibrosis
- Cystic fibrosis testing in pregnancy
- Talk to a pediatrician online