Doctor insights on:
Absent Pulmonary Valve In Children
A valve is a structure that regulates the direction of flow. The heart is a special kind of pump. It moves blood by squeezing and relaxing. There are 4 chambers and each chamber has a valve. This keeps blood from moving backwards when the heart squeezes. When a chamber squeezes it lets the blood move forward but when the chamber is relaxed it prevents the blood from ...Read more
Depends: Pulmonary valve atresia causes intense cyanosis and possibly respiratory distress. An absent pulmonary valve (tetralogy of fallot with absent pulmonary valve syndrome) presents with a heart murmur and respiratory distress. They usually have very dilated pulmonary arteries that compress the airways. ...Read more
Rare CHD: A rare congenital heart defect. The pulmonary valve doesn’t form and not enough blood can flow to the lungs to get oxygen; only through the PDA (patent ductus arteriosus). It often occurs as part of a condition called tetralogy of fallot. There is usually a hole between the left and right ventricles of the heart (ventricular septal defect). Surgery as a newborn is required. ...Read more
Absent pulmonary: Absent pulmonary valve is a congenital defect (occurring at birth). The pulmonary valve of the heart is absent or poorly formed. It can occur as a single defect or as the part of a complex congenital heart condition such as Tetralogy of Fallot. ...Read more
Rare defect: Absent pulmonary valve syndrome is a rare congenital heart defect. Some of the features are similar to tetralogy of fallot. An important difference in most babies with absent pulmonary valve syndrome is that the pulmonary arteries are very large, and often associated with problems with the airways. Surgery is required to repair the problems in the heart and repair the pulmonary arteries. ...Read more
ACHD - National Org: I think your best source of both information and the ability to connect with others with VSD/absent pulmonary valve is the American Congenital Heart Disease Association. (www. Achaheart. Org) website. They will have their annual meeting in Chicago Sept 5th-7th and much of it revolves around patients and their families. I have spoke at it before and it is an excellent meeting. Please check it out. ...Read more
Respiratory distress: Absent pulmonary valve syndrome is a rare form of congenital heart disease. There are some features that are similar to tetralogy of fallot. Absent pulmonary valve syndrome is different than pulmonary valve atresia. Corrective surgery is required. Typically, the dominant feature early is respiratory distress due to compression of the trachea and bronchi by enlarged pulmonary arteries. ...Read more
Probably none needed: If born this way, there probably is nothing that absolutely needs to be done because of an absent pulmonic valve per se. The valve adds to efficient function of the "right" (vs. Left) sided heart chambers, but the heart may compensate by itself. Any active intervention may be fraught with more risk than benefit, but consulting a pediatric cardiologist is prudent to confirm this & get best advice. ...Read more
When I was 8yrs old, my pulmonary valve was removed, not replaced, from stenosis. How common is this?
Incidence: This anomaly occurs in about 8 of every 10, 000 people (live births). ...Read more
Tof corrected 20 years back, now pulmonary valve to be replaced with bovine valve. Is there any other option. Which is the best valve option.
Talk to your doctor: This is the role your doctor should be taking- talk to you about the pros and cons on different options. If you don't trust his judgment, then you need to get a second opinion. For example, if you were a muslim, then a pork valve would not be an option for you regardless how good it may be. ...Read more
Pulmonary stenosis: Treatment for pulmonary valve stenosis varies depending upon the severity of stenosis and symptoms, and whether this is an isolated finding or there are other comorbid issues. Generally patients with mild to moderate stenosis may not require intervention, whereas patients with moderate to severe stenosis might require a catheter -or surgical-based approach to open up the narrowing. ...Read more
Pulmonary stenosis: There are a number of variables that pediatric cardiologists and heart surgeons take into consideration when determining how to approach pulmonary valve stenosis in a neonate. Generally speaking, a catheter-based approach is desirable to avoid surgery, and may be attempted first provided that the anatomy and other patient factors are amenable to that. ...Read more
Valve in the heart: The heart has 4 chambers. The right ventricle is the pumping chamber whic h pushes blood into the lungs so oxygen can be put into the blood. When the right ventricle squeezes, the pulmonary valve opens and blood flows into the lungs. When the right ventricle relaxes to fill, the pulmonary valve closes so blood can't flow backwards back into the heart. ...Read more
I can try: The pulmonary valve keeps blood from flowing back into your heart as it is pumped out into the lungs. I'm not sure what "mobile" means in this context, though my sense is that's what it should be - freely opening and closing. The increased flow velocity means the blood is moving faster than expected across the valve. If you are having any heart or lung symptoms, I'd see your doctor. ...Read more
No: Pulmonary valve stenosis may be mild and remain so for many years, but it does not go away without treatment. ...Read more
Depends: Depends on age, size of infundibulum, pulmonary annulus, tricuspid or bicuspid valve or degree of pulmonary atresia, primary or redo after previous congenital cardiac surgical repair. If it is a newborn and the annulus size is good and magoon ratio good, simple balloon angioplasty can be considered. Later on stented bioprosthesis can be considered. Otherwise pulmonary homograft at birth may be need. ...Read more
Pulmonary stenosis: Mild to moderate pulmonary valve stenosis generally has a good prognosis. Mild pulmonary valve stenosis usually does not progress, but moderate pulmonary valve stenosis may worsen over time and require surgery. Treatment is generally highly successful allowing people to live high quality lives provided that they do not have other comorbid problems. ...Read more
See below: Structural differences are minimal. They are both fibrous and usually have three cusps. The tricuspid is anchored to tiny muscles called papillary muscles. The functional differences are more relevant. The tricuspid regulates blood flow between the right atrium and the right ventricle, while the pulmonary valve stands between the right ventricle and the pulmonary artery. ...Read more
I am using artificial pulmonary valve (bio) and have to do another pvr surgeries, is it possible for me to do pvr using catheter?
Indication?: Assuming an adult patient, it would be important to determine if replacement is truly necessary. If the valve is very tight and creating right heart failure or low output syndrome (quite rare), valvuloplasty or removal without replacement may suffice. If the valve is infected, other complications may be present. Best left to the attending cardiologist and consulting surgeon. ...Read more
Discuss with MD: You really need to discuss this with your surgeon. It is way too involved of a discussion for this kind of board. ...Read more
My eight month old daughter was just diagnosed with pulmonary valve stenosis. Can you tell me more about this?
Severity?: It is a congenital defect in which the valve that allows blood to pass out of the right ventricle into the pulmonary artery and lungs doesn't open properly. If mild, it causes no symptoms. If severe, it can strain the right ventricle which eventually will fail. The valve can be stretched open with a catheter (valvuloplasty) or replaced with surgery. ...Read more
What do you suggest if my eight month old daughter was just diagnosed with pulmonary valve stenosis. Anyone have an experience with this?
Pulmonary stenosis: She needs to be evaluated by a Pediatric Cardiologist. Then you need to get a discussion from that Doc. ...Read more
There are many: Possible reasons for "coding" unassociated with open heart surgery. Any patient considered for pulmonary valve replacement will be appropriately evaluated prior to surgery to optimize their postoperative recovery. Even with that preparation there is always a chance that bad things can happen. ...Read more
Get the flu shot: Of course after a pulmonary valve replacement or repair, your child is going to be in the cardiac ICU for a period of time and on the floor. There's going to be ample time to get advice on what to do. Make sure they get the flu shot, and more than likely your child is going to need antibiotics before dental cleanings and certain medical procedures. Make sure they always get that taken care of. ...Read more
The heart has 4 chambers. The right ventricle is the pumping chamber whic h pushes blood into the lungs so oxygen can be put into the blood. When the right ventricle squeezes, the pulmonary valve opens and blood flows into the lungs. When the right ventricle relaxes to fill, the pulmonary valve closes so blood can't flow backwards ...Read more