Disease-specific reference equations for lung function in patients with cystic fibrosis.
American Journal of Respiratory and Critical Care Medicine
Pseudomonas aeruginosa serology and risk for re-isolation in the EPIC trial.
J. Cyst. Fibros., Aug (2012)
Exome sequencing of extreme phenotypes identifies DCTN4 as a modifier of chronic Pseudomonas aeruginosa infection in cystic fibrosis.
Nat. Genet., Aug;44(8):886-9 (2012)
Risk factors for age at initial Pseudomonas acquisition in the cystic fibrosis epic observational cohort.
J. Cyst. Fibros., Sep;11(5):446-53 (2012)
Feasibility of using pedometers to measure daily step counts in cystic fibrosis and an assessment of its responsiveness to changes in health state.
J. Cyst. Fibros., May;11(3):216-22 (2012)
Respiratory viruses in children with cystic fibrosis: viral detection and clinical findings.
Influenza Other Respi Viruses., May;6(3):218-23 (2012)
Comparative efficacy and safety of 4 randomized regimens to treat early Pseudomonas aeruginosa infection in children with cystic fibrosis.
Arch Pediatr Adolesc Med., Sep;165(9):847-56 (2011)
Initial Pseudomonas aeruginosa treatment failure is associated with exacerbations in cystic fibrosis.
Pediatr. Pulmonol., Feb;47(2):125-34 (2012)
Pseudomonas aeruginosa antibiotic susceptibility during long-term use of aztreonam for inhalation solution (AZLI).
J. Antimicrob. Chemother., Oct;66(10):2398-404 (2011)
Randomized trial of biofilm testing to select antibiotics for cystic fibrosis airway infection.
Pediatr. Pulmonol., Feb;46(2):184-92 (2011)
An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis.
Pediatr. Pulmonol., Nov;45(11):1121-34 (2010)
Baseline characteristics and factors associated with nutritional and pulmonary status at enrollment in the cystic fibrosis EPIC observational cohort.
Pediatr. Pulmonol., Sep;45(9):934-44 (2010)
Return of FEV1 after pulmonary exacerbation in children with cystic fibrosis.
Pediatr. Pulmonol., Feb;45(2):127-34 (2010)
Early anti-pseudomonal acquisition in young patients with cystic fibrosis: rationale and design of the EPIC clinical trial and observational study'.
Contemp Clin Trials., May;30(3):256-68 (2009)
Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis.
Chest., May;135(5):1223-32 (2009)
Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders.
Genet. Med., Dec;10(12):851-68 (2008)
Impact of Pseudomonas and Staphylococcus infection on inflammation and clinical status in young children with cystic fibrosis.
J. Pediatr., Feb;154(2):183-8 (2009)
Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis.
Am. J. Respir. Crit. Care Med., Nov;178(9):921-8 (2008)
Pharmacogenomic testing to prevent aminoglycoside-induced hearing loss in cystic fibrosis patients: potential impact on clinical, patient, and economic outcomes.
Genet. Med., Oct;9(10):695-704 (2007)
A phase 2 study of aztreonam lysine for inhalation to treat patients with cystic fibrosis and Pseudomonas aeruginosa infection.
Pediatr. Pulmonol., Jan;43(1):47-58 (2008)
Oral corticosteroid therapy in cystic fibrosis patients hospitalized for pulmonary exacerbation: a pilot study.
Chest., Oct;132(4):1212-8 (2007)
Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
Pediatr. Pulmonol., Jul;42(7):610-23 (2007)
Selection for Staphylococcus aureus small-colony variants due to growth in the presence of Pseudomonas aeruginosa.
Proc. Natl. Acad. Sci. U.S.A., Dec;103(52):19890-5 (2006)
Microbiology, safety, and pharmacokinetics of aztreonam lysinate for inhalation in patients with cystic fibrosis.
Pediatr. Pulmonol., Jul;41(7):656-65 (2006)
Prevalence of neutralizing antibodies against adeno-associated virus (AAV) types 2, 5, and 6 in cystic fibrosis and normal populations: Implications for gene therapy using AAV vectors.
Hum. Gene Ther., Apr;17(4):440-7 (2006)
Lipoid pneumonia due to Mexican folk remedies: cultural barriers to diagnosis.
Arch Pediatr Adolesc Med., Nov;159(11):1043-8 (2005)
Use of Pseudomonas biofilm susceptibilities to assign simulated antibiotic regimens for cystic fibrosis airway infection.
J. Antimicrob. Chemother., Nov;56(5):879-86 (2005)
The prevalence of ibuprofen-sensitive asthma in children: a randomized controlled bronchoprovocation challenge study.
J. Pediatr., Aug;147(2):233-8 (2005)
Cystic fibrosis lung disease: genetic influences, microbial interactions, and radiological assessment.
Pediatr Radiol., Aug;35(8):739-57 (2005)
Randomized, double-blind, placebo-controlled, dose-escalating study of aerosolized interferon gamma-1b in patients with mild to moderate cystic fibrosis lung disease.
Pediatr. Pulmonol., Mar;39(3):209-18 (2005)
Pathophysiology and management of pulmonary infections in cystic fibrosis.
Am. J. Respir. Crit. Care Med., Oct;168(8):918-51 (2003)
Pseudomonas acquisition in young patients with cystic fibrosis: pathophysiology, diagnosis, and management.
Curr Opin Pulm Med., Nov;9(6):492-7 (2003)
The role of group B streptococci beta-hemolysin expression in newborn lung injury.
Adv. Exp. Med. Biol., 418:627-30 (1997)
Lung hyaluronan decreases during group B streptococcal pneumonia in neonatal piglets.
Am. J. Respir. Crit. Care Med., May;153(5):1567-70 (1996)
Diaphragmatic failure during group B streptococcal sepsis in piglets: the role of thromboxane A2.
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Effect of nitric oxide synthase inhibition during group B streptococcal sepsis in neonatal piglets.
Pediatr. Res., Dec;36(6):776-83 (1994)
Effect of amrinone during group B Streptococcus-induced pulmonary hypertension in piglets.
Pediatr. Pulmonol., Nov;16(5):303-10 (1993)
Efficacy and safety of short-term administration of aerosolized recombinant human deoxyribonuclease in patients with cystic fibrosis.
Am. Rev. Respir. Dis., Jul;148(1):145-51 (1993)
Efficacy of aerosolized tobramycin in patients with cystic fibrosis.
N. Engl. J. Med., Jun;328(24):1740-6 (1993)
Effect of inhaled nitric oxide during group B streptococcal sepsis in piglets.
Am. Rev. Respir. Dis., May;147(5):1080-6 (1993)
Lung vascular responses and VA/Q matching after chronic hypoxia in neonatal piglets.
J. Dev. Physiol., Apr;19(4):157-63 (1993)
Group B streptococci invade endothelial cells: type III capsular polysaccharide attenuates invasion.
Infect. Immun., Feb;61(2):478-85 (1993)
Effect of group B streptococcal sepsis on diaphragmatic function in young piglets.
Pediatr. Res., Jan;33(1):10-4 (1993)
Group B streptococcal sepsis in piglets: effect of combined pentoxifylline and indomethacin pretreatment.
Pediatr. Res., Mar;31(3):222-7 (1992)
Effect of pentoxifylline on cytokine- and eicosanoid-induced acute pulmonary hypertension in piglets.
Pediatr. Res., Feb;31(2):163-9 (1992)
Group B streptococcus has no effect on piglet diaphragmatic force generation.
Am. Rev. Respir. Dis., Feb;145(2 Pt 1):471-5 (1992)
Group B streptococcus induces tumor necrosis factor in neonatal piglets. Effect of the tumor necrosis factor inhibitor pentoxifylline on hemodynamics and gas exchange.
Am. Rev. Respir. Dis., Mar;143(3):598-604 (1991)
Respiratory mechanics of the piglet during the first month of life.
Pediatr. Pulmonol., 11(4):294-301 (1991)
Lung function in children following empyema.
Am. J. Dis. Child., Dec;144(12):1337-42 (1990)
Tumor necrosis factor-induced neonatal pulmonary hypertension: effects of dazmegrel pretreatment.
Pediatr. Res., May;27(5):466-71 (1990)
Regional pulmonary blood flow in piglets during group B streptococcal bacteremia.
Am. Rev. Respir. Dis., May;141(5 Pt 1):1209-13 (1990)
Isogenic group B streptococci devoid of capsular polysaccharide or beta-hemolysin: pulmonary hemodynamic and gas exchange effects during bacteremia in piglets.
Pediatr. Res., Sep;26(3):241-5 (1989)
Effects of respiratory alkalosis on thromboxane-induced pulmonary hypertension in piglets.
Pediatr. Res., Nov;24(5):558-62 (1988)
Bronchopulmonary dysplasia. Survival after prolonged mechanical ventilation.
Am. J. Dis. Child., Jul;142(7):721-5 (1988)
Thromboxane-associated pulmonary hypertension during three types of gram-positive bacteremia in piglets.
Pediatr. Res., Jun;23(6):553-6 (1988)
Neonatal group B streptococcal sepsis: effects of late treatment with dazmegrel.
Pediatr. Res., Apr;23(4):352-6 (1988)
Hypoxic pulmonary vasoconstriction during and after infusion of group B Streptococcus in neonatal piglets. Vascular pressure-flow analysis.
Am. Rev. Respir. Dis., Apr;137(4):774-8 (1988)